Ectopia Cordis Associated with Pentalogy of Cantrell-A Case Report

被引：5

作者：

Madi, Jose Mauro ^{[1
]}

Festugatto, Jose Roberto ^{[2
]}

Rizzon, Matheus ^{[2
]}

Agostini, Ana Paula ^{[3
]}

de Araujo, Breno Fauth ^{[3
]}

Rahmi Garcia, Rosa Maria ^{[4
]}

机构：

[1] Univ Caxias do Sul, Dept Obstet & Gynecol, Fac Med, Ave Prof Antonio Vignolli 255,Campus Univ, BR-95001970 Caxias Do Sul, RS, Brazil

[2] Univ Caxias do Sul, Dept Radiol, Hosp Geral Caxias do Sul, Caxias Do Sul, RS, Brazil

[3] Univ Caxias do Sul, Dept Pediat & Neonatol, Fac Med, Caxias Do Sul, RS, Brazil

[4] Univ Caxias do Sul, Dept Endocrinol, Fac Med, Caxias Do Sul, RS, Brazil

来源：

REVISTA BRASILEIRA DE GINECOLOGIA E OBSTETRICIA | 2019年 / 41卷 / 05期

关键词：

ectopia cordis; pentalogy of Cantrell; abdominal wall defects; congenital heart defects; umbilical hernia; PRENATAL-DIAGNOSIS; CONGENITAL-DEFECTS; ABDOMINAL-WALL; OF-CANTRELL; DIAPHRAGM; PERICARDIUM; OMPHALOCELE; STERNUM; INFANT;

D O I：

10.1055/s-0039-1679878

中图分类号：

R71 [妇产科学];

学科分类号：

100211 ;

摘要：

Pentalogy of Cantrell (PC) is a rare congenital anomaly characterized by changes in the mesodermal median structures and congenital heart disease, often with a poor prognosis. In 1958, Cantrell et al(2) defined the full spectrum of the syndrome with the following anomalies: defects of the anterior diaphragm, of the lower part of the sternum, of the supraumbilical region and the abdominal wall, of the diaphragmatic pericardium, and various intracardiac congenital abnormalities. The present report describes a case of ectopia cordis associated with PC and the importance of the participation of a multidisciplinary team in the treatment of this condition.

引用

页码：352 / 356

页数：5

共 32 条

[1] Diagnosis of pentalogy of Cantrell by three-dimensional ultrasound in third trimester of pregnancy - A case report [J].