Arrhythmogenic Right Ventricular Cardiomyopathy

被引:1
|
作者
Dolkar, Tsering [1 ]
Nway, Nway [1 ]
Hamad, Abubaker M. [2 ]
Jain, Hardik [3 ]
Dufresne, Alix [4 ]
机构
[1] One Brooklyn Hlth, Internal Med, Interfaith Med Ctr, New York, NY 11213 USA
[2] Mem Hosp Converse Cty, Med, Douglas, AR USA
[3] Saba Univ, Internal Med, Sch Med, Devens, MA USA
[4] One Brooklyn Hlth Interfaith Med Ctr, Cardiol, New York, NY USA
关键词
myocardial fibro fatty tissue; echo cardiogram; cardiomyopathy; right ventricle; arrhythmogenic; DIAGNOSIS;
D O I
10.7759/cureus.31446
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Arrhythmogenic right ventricular cardiomyopathy (ARVC), formerly called arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/ARVC), is a myocardial structural abnormality disease with clinical presentation of cardiac arrhythmia. It is characterized by the replacement of the myocardium with fibrofatty tissue. We present a case of a young male who met two major criteria for definite diagnosis of ARVC: early transition inverted t waves in lead V1-V4 and MRI showed right ventricle (RV) dyskinesia with RV ejection fraction (EF) < 40%, both satisfying the two major criteria of EKG and MRI required for definitive diagnosis.
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页数:6
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