A Rare Case of Synovial Sarcoma Involving the Brachial Plexus, Treated with Wide Local Excision and Reconstructed with Sural Nerve Grafts
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作者:
Atodaria, Kuldeepsinh Pradipkumar
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Bharat Canc Hosp & Res Ctr, Surat Bardoli Rd,Opp HP Petr Pump, Surat 395010, Gujarat, IndiaBharat Canc Hosp & Res Ctr, Surat Bardoli Rd,Opp HP Petr Pump, Surat 395010, Gujarat, India
Atodaria, Kuldeepsinh Pradipkumar
[1
]
KishorkumarVithalani, Nikunj
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机构:
New Civil Hosp, Ring Rd, Surat 395001, Gujarat, IndiaBharat Canc Hosp & Res Ctr, Surat Bardoli Rd,Opp HP Petr Pump, Surat 395010, Gujarat, India
KishorkumarVithalani, Nikunj
[2
]
Bharambe, Atul Gajendra
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New Civil Hosp, Ring Rd, Surat 395001, Gujarat, IndiaBharat Canc Hosp & Res Ctr, Surat Bardoli Rd,Opp HP Petr Pump, Surat 395010, Gujarat, India
Bharambe, Atul Gajendra
[2
]
Mishra, Bharat Chandra
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New Civil Hosp, Ring Rd, Surat 395001, Gujarat, IndiaBharat Canc Hosp & Res Ctr, Surat Bardoli Rd,Opp HP Petr Pump, Surat 395010, Gujarat, India
Mishra, Bharat Chandra
[2
]
Chauhan, Keshvi Mahendrasinh
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机构:
Bharat Canc Hosp & Res Ctr, Surat Bardoli Rd,Opp HP Petr Pump, Surat 395010, Gujarat, IndiaBharat Canc Hosp & Res Ctr, Surat Bardoli Rd,Opp HP Petr Pump, Surat 395010, Gujarat, India
Chauhan, Keshvi Mahendrasinh
[1
]
机构:
[1] Bharat Canc Hosp & Res Ctr, Surat Bardoli Rd,Opp HP Petr Pump, Surat 395010, Gujarat, India
[2] New Civil Hosp, Ring Rd, Surat 395001, Gujarat, India
Synovial sarcoma;
Brachial plexus;
Head and neck carcinomas;
Nerve reconstruction;
NECK;
HEAD;
SURVIVAL;
D O I:
10.1007/s13193-019-00883-z
中图分类号:
R73 [肿瘤学];
学科分类号:
100214 ;
摘要:
This is a case report of monophasic synovial sarcoma involving right brachial plexus. Clinical and radiological examination is not very useful in diagnosis. Histopathology showed spindle cells with occasional mitotic figures. Immunohistochemistry showed positivity for EMA, S-100, Mic-2, Bcl-2, Calponin, TLE-1 and CD-56. Chromosomal translocation t (X;18) (p11.2;q11.2) and chimeric fusion proteins SYT/SSX1 or SYT/SSX2 are formed. Wide local excision of the tumour with involved brachial plexus and later reconstruction of the brachial plexus using sural nerve grafts was done. Patient showed full recovery. Wide excision and radiotherapy is the accepted mode of treatment.