Echocardiographic Segmental Analysis in Patients With an Atrioventricular Criss-Cross

The aim of this study was to describe the echocardiographic characteristics of patients with an atrioventricular criss-cross who underwent segmental cardiac morphological analysis. The study involved five patients with a criss-cross heart (0.6% of the studies). The patients' average age was 6 years and 3 months. All patients presented with situs solitus. Three had a discordant atrioventricular connection and two had a concordant connection. In addition, four patients had a ventriculoarterial connection with a double-outlet right ventricle while one had a concordant connection. Two patients had superior-inferior ventricles. Other associated lesions included ventricular septal defect in all patients, pulmonary stenosis, persistent ductus arteriosus and atrial septal defect in three, pulmonary perforation in one, and a hypoplastic aortic arch in one. In these patients, segmental analysis can be carried out satisfactorily using transthoracic echocardiography.