Current Concept of IgG4-Related Disease

被引：19

作者：

Okazaki, Kazuichi ^{[1
,2
]}

Umehara, Hisanori ^{[3
]}

机构：

[1] Kansai Med Univ, Dept Gastroenterol & Hepatol, Osaka, Japan

[2] Kansai Med Univ, Dept Internal Med 3, Div Gastroenterol & Hepatol, Shinmachi, Hirakata, Osaka 5731197, Japan

[3] Hayashi Hosp, Northern Cty Ctr RA & Autoimmune Dis, Fukui, Japan

来源：

IGG4-RELATED DISEASE | 2017年 / 401卷

关键词：

COMPLICATING AUTOIMMUNE PANCREATITIS; IGG4-POSITIVE PLASMA-CELLS; SCLEROSING CHOLANGITIS; MULTIFOCAL FIBROSCLEROSIS; DIAGNOSTIC-CRITERIA; RETROPERITONEAL FIBROSIS; INFLAMMATORY PSEUDOTUMOR; CLOSE RELATIONSHIP; SYSTEMIC-DISEASE; THYROIDITIS;

D O I：

10.1007/82_2016_47

中图分类号：

R57 [消化系及腹部疾病];

学科分类号：

摘要：

IgG4-related disease (IgG4-RD) is a fibroinflammatory disease of unknown etiology, which is characterized by a tendency to form tumefactive lesions, increased serum levels of IgG4, and massive infiltration of IgG4-positive plasma cells with storiform fibrosis and/or obliterative phlebitis. Patients with IgG4-RD have frequently multiorgan involvements such as the pancreas, biliary tree, salivary glands, periorbital tissues, kidneys, lungs, lymph nodes, and retroperitoneum. IgG4-RD mainly affects middle-aged to elderly men except for involvement in lachrymal and salivary glands, so-called Mikulicz's disease. The clinical manifestations of IgG4-RD depend on individually involved organs and respond well to steroid, but the prognosis still remains unclear. Some patients develop serious complications such as obstructive jaundice due to hepatic, gall-bladder, or pancreatic lesions; hydronephrosis due to retroperitoneal fibrosis; or respiratory symptoms due to pulmonary lesions. Nomenclatures of individual organ manifestation of IgG4-RD have been internationally consented.

引用

页码：1 / 17

页数：17

共 63 条

[1] Diagnosis of autoimmune pancreatitis: The Mayo Clinic experience [J].

Chari, Suresh T. ;

Smyrk, Thomas C. ;

Levy, Michael J. ;

Topazian, Mark D. ;

Takahashi, Naoki ;

Zhang, Lizhi ;

Clain, Jonathan E. ;

Pearson, Randall K. ;

Petersen, Bret T. ;

Vege, Santhi Swaroop ;

Farnell, Michael B. .

CLINICAL GASTROENTEROLOGY AND HEPATOLOGY, 2006, 4 (08) :1010-1016

[2] Histopathologic and Clinical Subtypes of Autoimmune Pancreatitis The Honolulu Consensus Document [J].

Chari, Suresh T. ;

Kloeppel, Guenter ;

Zhang, Lizhi ;

Notohara, Kenji ;

Lerch, Markus M. ;

Shimosegawa, Tooru .

PANCREAS, 2010, 39 (05) :549-554

[3] IgG4-related Sclerosing Mastitis: Description of a New Member of the IgG4-related Sclerosing Diseases [J].

Cheuk, Wah ;

Chan, Alexander C. L. ;

Lam, Wai-Lung ;

Chow, Sheung-Ming ;

Crowley, Peter ;

Lloydd, Richard ;

Campbell, Ian ;

Thorburn, Murray ;

Chan, John K. C. .

AMERICAN JOURNAL OF SURGICAL PATHOLOGY, 2009, 33 (07) :1058-1064

[4] FAMILIAL MULTIFOCAL FIBROSCLEROSIS - FINDINGS SUGGESTING THAT RETROPERITONEAL FIBROSIS MEDIASTINAL FIBROSIS SCLEROSING CHOLANGITIS RIEDELS THYROIDITIS AND PSEUDOTUMOR OF ORBIT MAY BE DIFFERENT MANIFESTATIONS OF A SINGLE DISEASE [J].

COMINGS, DE ;

SKUBI, KB ;

VANEYES, J ;

MOTULSKY, AG .

ANNALS OF INTERNAL MEDICINE, 1967, 66 (05) :884-+

[5] Consensus statement on the pathology of IgG4-related disease [J].

Deshpande, Vikram ;

Zen, Yoh ;

Chan, John K. ;

Yi, Eunhee E. ;

Sato, Yasuharu ;

Yoshino, Tadashi ;

Kloeppel, Guenter ;

Heathcote, J. Godfrey ;

Khosroshahi, Arezou ;

Ferry, Judith A. ;

Aalberse, Rob C. ;

Bloch, Donald B. ;

Brugge, William R. ;

Bateman, Adrian C. ;

Carruthers, Mollie N. ;

Chari, Suresh T. ;

Cheuk, Wah ;

Cornell, Lynn D. ;

Fernandez-Del Castillo, Carlos ;

Forcione, David G. ;

Hamilos, Daniel L. ;

Kamisawa, Terumi ;

Kasashima, Satomi ;

Kawa, Shigeyuki ;

Kawano, Mitsuhiro ;

Lauwers, Gregory Y. ;

Masaki, Yasufumi ;

Nakanuma, Yasuni ;

Notohara, Kenji ;

Okazaki, Kazuich ;

Ryu, Ji Kon ;

Saeki, Takako ;

Sahani, Dushyant V. ;

Smyrk, Thomas C. ;

Stone, James R. ;

Takahira, Masayuki ;

Webster, George J. ;

Yamamoto, Motohisa ;

Zamboni, Giuseppe ;

Umehara, Hisanori ;

Stone, John H. .

MODERN PATHOLOGY, 2012, 25 (09) :1181-1192

[6] Immunoglobulin G4-associated cholangitis: Clinical profile and response to therapy [J].

Ghazale, Amaar ;

Chari, Suresh T. ;

Zhang, Lizhi ;

Smyrk, Thomas C. ;

Takahashi, Naoki ;

Levy, Michael J. ;

Topazian, Mark D. ;

Clain, Jonathan E. ;

Pearson, Randall K. ;

Petersen, Bret T. ;

Vege, Santhi Swaroop ;

Lindor, Keith ;

Farnell, Michael B. .

GASTROENTEROLOGY, 2008, 134 (03) :706-715

[7] Diagnostic criteria for IgG4-related ophthalmic disease [J].

Goto, Hiroshi ;

Takahira, Masahiro ;

Azumi, Atsushi .

JAPANESE JOURNAL OF OPHTHALMOLOGY, 2015, 59 (01) :1-7

[8] Hydronephrosis associated with retroperitoneal fibrosis and sclerosing pancreatitis [J].

Hamano, H ;

Kawa, S ;

Ochi, Y ;

Unno, H ;

Shiba, N ;

Wajiki, M ;

Nakazawa, K ;

Shimojo, H ;

Kiyosawa, K .

LANCET, 2002, 359 (9315) :1403-1404

[9] High serum IgG4 concentrations in patients with sclerosing pancreatitis. [J].

Hamano, H ;

Kawa, S ;

Horiuchi, A ;

Unno, H ;

Furuya, N ;

Akamatsu, T ;

Fukushima, M ;

Nikaido, T ;

Nakayama, K ;

Usuda, N ;

Kiyosawa, K .

NEW ENGLAND JOURNAL OF MEDICINE, 2001, 344 (10) :732-738

[10] Immunoglobulin G4-related lymphoplasmacytic sclerosing cholangitis that mimics infiltrating hilar cholangiocarcinoma: part of a spectrum of autoimmune pancreatitis? [J].

Hamano, H ;

Kawa, S ;

Uehara, T ;

Ochi, Y ;

Takayama, M ;

Komatsu, K ;

Muraki, T ;

Umino, J ;

Kiyosawa, K ;

Miyagawa, S .

GASTROINTESTINAL ENDOSCOPY, 2005, 62 (01) :152-157

← 1 2 3 4 5 6 7 →