Pulmonary alveolar proteinosis in adenosine deaminase-deficient mice

被引:12
|
作者
Dhanju, Rupreet [1 ,2 ]
Min, Weixian [1 ]
Ackerley, Cameron [3 ]
Cimpean, Lorand [4 ]
Palaniyar, Nades [5 ]
Roifman, Chaim M. [4 ]
Grunebaum, Eyal [1 ,4 ]
机构
[1] Univ Toronto, Hosp Sick Children, Dev & Stem Cell Biol Program, Toronto, ON M5G 1X8, Canada
[2] Univ Toronto, Fac Med, Inst Med Sci, Toronto, ON M5G 1X8, Canada
[3] Univ Toronto, Hosp Sick Children, Dept Pathobiol & Lab Med, Toronto, ON M5G 1X8, Canada
[4] Univ Toronto, Hosp Sick Children, Div Immunol & Allergy, Toronto, ON M5G 1X8, Canada
[5] Univ Toronto, Hosp Sick Children, Physiol & Expt Med Program, Toronto, ON M5G 1X8, Canada
基金
加拿大健康研究院;
关键词
ABNORMALITIES; CONSEQUENCES; INFLAMMATION;
D O I
10.1016/j.jaci.2013.11.029
中图分类号
R392 [医学免疫学];
学科分类号
100102 ;
摘要
[No abstract available]
引用
收藏
页码:1467 / +
页数:9
相关论文
共 50 条
  • [21] Hepatic Manifestations in Adenosine Deaminase-Deficient Severe Combined Immune Deficiency
    Lingala, Shilpa
    Garabedian, Elizabeth
    Candotti, Fabio
    Kleiner, David E.
    Wilkins, Kenneth J.
    Heller, Theo
    Koh, Christopher
    HEPATOLOGY, 2015, 62 : 1045A - 1045A
  • [22] Update on gene therapy for adenosine deaminase-deficient severe combined immunodeficiency
    Ferrua, Francesca
    Brigida, Immacolata
    Aiuti, Alessandro
    CURRENT OPINION IN ALLERGY AND CLINICAL IMMUNOLOGY, 2010, 10 (06) : 551 - 556
  • [23] PULMONARY ALVEOLAR PROTEINOSIS IN SCID MICE
    JENNINGS, VM
    DILLEHAY, DL
    WEBB, SK
    BROWN, LAS
    AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY, 1995, 13 (03) : 297 - 306
  • [24] 1-METHYLADENINE IN URINE OF AN ADENOSINE DEAMINASE-DEFICIENT ADULT WITHOUT IMMUNODEFICIENCY
    MILLS, GC
    BIOCHEMICAL MEDICINE AND METABOLIC BIOLOGY, 1989, 42 (03): : 240 - 247
  • [25] HUMAN ADENOSINE-DEAMINASE AND ITS BINDING-PROTEIN IN NORMAL AND ADENOSINE DEAMINASE-DEFICIENT FIBROBLAST CELL STRAINS
    DADDONA, PE
    FROHMAN, MA
    KELLEY, WN
    JOURNAL OF BIOLOGICAL CHEMISTRY, 1980, 255 (12) : 5681 - 5687
  • [26] Busulfan Pharmacokinetics in Adenosine Deaminase-Deficient Severe Combined Immunodeficiency Gene Therapy
    Bradford, Kathryn L.
    Liu, Siyu
    Krajinovic, Maja
    Ansari, Marc
    Garabedian, Elizabeth
    Tse, John
    Wang, Xiaoyan
    Shaw, Kit L.
    Gaspar, H. Bobby
    Candotti, Fabio
    Kohn, Donald B.
    BIOLOGY OF BLOOD AND MARROW TRANSPLANTATION, 2020, 26 (10) : 1819 - 1827
  • [27] A PHENOTYPICALLY NORMAL REVERTANT OF AN ADENOSINE DEAMINASE-DEFICIENT LYMPHOBLAST CELL-LINE
    UBERTI, J
    PETERSON, WD
    LIGHTBODY, JJ
    JOHNSON, RM
    JOURNAL OF IMMUNOLOGY, 1983, 130 (06): : 2866 - 2870
  • [28] Gene therapy for the treatment of adenosine deaminase-deficient severe combined immune deficiency
    Sokolic, Robert
    Candotti, Fabio
    EXPERT OPINION ON ORPHAN DRUGS, 2017, 5 (06): : 477 - 485
  • [29] ESTABLISHMENT AND CHARACTERIZATION OF ADENOSINE DEAMINASE-DEFICIENT HUMAN T-CELL LINES
    KOHN, DB
    MITSUYA, H
    BALLOW, M
    SELEGUE, JE
    BARANKIEWICZ, J
    COHEN, A
    GELFAND, E
    ANDERSON, WF
    BLAESE, RM
    JOURNAL OF IMMUNOLOGY, 1989, 142 (11): : 3971 - 3977
  • [30] Autoantibody-Mediated Pulmonary Alveolar Proteinosis in Rasgrp1-Deficient Mice
    Ferretti, Andrew
    Fortwendel, Jarrod R.
    Gebb, Sarah A.
    Barrington, Robert A.
    JOURNAL OF IMMUNOLOGY, 2016, 197 (02): : 470 - 479