Skin Involvement in Atypical Hemolytic Uremic Syndrome

被引：24

作者：

Ardissino, Gianluigi ^{[1
]}

Tel, Francesca ^{[1
]}

Testa, Sara ^{[1
]}

Marzano, Angelo Valerio ^{[2
]}

Lazzari, Riccardo ^{[2
]}

Salardi, Stefania ^{[1
]}

Edefonti, Alberto ^{[1
]}

机构：

[1] Osped Maggiore Policlin, Ctr HUS Prevent Control & Management, Fdn IRCCS Ca Granda, I-20122 Milan, Italy

[2] Osped Maggiore Policlin, Dermatol Unit, Fdn IRCCS Ca Granda, I-20122 Milan, Italy

来源：

AMERICAN JOURNAL OF KIDNEY DISEASES | 2014年 / 63卷 / 04期

关键词：

Haemolytic uremic syndrome; skin; eculizumab; thrombotic microangiopathy; plasma exchange; case report; MUTATIONS;

D O I：

10.1053/j.ajkd.2013.09.020

中图分类号：

R5 [内科学]; R69 [泌尿科学（泌尿生殖系疾病）];

学科分类号：

1002 ; 100201 ;

摘要：

Skin involvement in atypical hemolytic uremic syndrome (aHUS) is very uncommon and therefore often unrecognized as a specific symptom of aHUS. We describe 3 cases of patients with aHUS who developed skin lesions that completely recovered when disease-specific treatment was established. These cases suggest that in individuals with aHUS, when skin lesions of unknown origin occur, the possibility that they are due to thrombotic microangiopathy should be considered. (C) 2014 by the National Kidney Foundation, Inc.

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收藏

页码：652 / 655

页数：4

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