von Willebrand factor cleaved from endothelial cells by ADAMTS13 remains ultralarge in size

被引:17
作者
Jin, S. -Y. [1 ,2 ]
Skipwith, C. G. [1 ,2 ]
Shang, D. [1 ,2 ]
Zheng, X. L. [1 ,2 ,3 ]
机构
[1] Childrens Hosp Philadelphia, Dept Pathol, Philadelphia, PA 19104 USA
[2] Childrens Hosp Philadelphia, Lab Med, Philadelphia, PA 19104 USA
[3] Univ Penn, Med Ctr, Philadelphia, PA 19104 USA
关键词
FACTOR MULTIMERS; SHEAR-STRESS; METALLOPROTEASE; PLASMA; CONFORMATION; PROTEOLYSIS; PROTEASE; REQUIRES; SURFACE; FLOW;
D O I
10.1111/j.1538-7836.2009.03570.x
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:1749 / 1752
页数:4
相关论文
共 50 条
  • [31] ADAMTS-13: double trouble for von Willebrand factor
    Lenting, P. J.
    Rastegarlari, G.
    JOURNAL OF THROMBOSIS AND HAEMOSTASIS, 2010, 8 (12) : 2775 - 2777
  • [32] Plasma ADAMTS13 activity and von Willebrand factor antigen and activity in patients with subarachnoid haemorrhage
    Kumar, Monisha
    Cao, Wenjing
    Pham, Huy P.
    Raju, Dheeraj
    Nawalinski, Kelsey
    Frangos, Suzanne
    Kung, David
    Zager, Eric E.
    Kasner, Scott E.
    Levine, Joshua M.
    Zheng, X. Long
    THROMBOSIS AND HAEMOSTASIS, 2017, 117 (04) : 691 - 699
  • [33] The function of ultra-large von Willebrand factor multimers in high shear flow controlled by ADAMTS13
    Reininger, A. J.
    HAMOSTASEOLOGIE, 2015, 35 (03): : 225 - 233
  • [34] Von Willebrand factor, ADAMTS13, and coronary microvascular obstruction: beautiful hypotheses, ugly facts
    De Caterina, Raffaele
    Madonna, Rosalinda
    CARDIOVASCULAR RESEARCH, 2016, 111 (03) : 169 - 171
  • [35] Oxidative modification of von Willebrand factor by neutrophil oxidants inhibits its cleavage by ADAMTS13
    Chen, Junmei
    Fu, Xiaoyun
    Wang, Yi
    Ling, Minhua
    McMullen, Brad
    Kulman, John
    Chung, Dominic W.
    Lopez, Jose A.
    BLOOD, 2010, 115 (03) : 706 - 712
  • [36] C1584 in von Willebrand factor is necessary for enhanced proteolysis by ADAMTS13 in vitro
    Keeney, S.
    Grundy, P.
    Collins, P. W.
    Bowen, D. J.
    HAEMOPHILIA, 2007, 13 (04) : 405 - 408
  • [37] Levels of von Willebrand factor antigen and von Willebrand factor cleaving protease (ADAMTS13) activity predict clinical events in chronic heart failure
    Gombos, Timea
    Mako, Veronika
    Cervenak, Laszlo
    Papassotiriou, Jana
    Kunde, Jan
    Harsfalvi, Jolan
    Forhecz, Zsolt
    Pozsonyi, Zoltan
    Borgulya, Gabor
    Janoskuti, Livia
    Prohaszka, Zoltan
    THROMBOSIS AND HAEMOSTASIS, 2009, 102 (03) : 573 - 580
  • [38] Preclinical Testing of Human Recombinant von Willebrand Factor: ADAMTS13 Cleavage Capacity in Animals as Criterion for Species Suitability
    Muchitsch, Eva-Maria
    Dietrich, Barbara
    Rottensteiner, Hanspeter
    Auer, Wilfried
    Nehrbass, Dirk
    Gritsch, Herbert
    Ehrlich, Hartmut J.
    Turecek, Peter L.
    Schwarz, Hans Peter
    SEMINARS IN THROMBOSIS AND HEMOSTASIS, 2010, 36 (05) : 522 - 528
  • [39] Role of calcium in regulating the intra- and extracellular cleavage of von Willebrand factor by the protease ADAMTS13
    Gogia, Shobhit
    Kelkar, Anju
    Zhang, Changjie
    Dayananda, Kannayakanahalli M.
    Neelamegham, Sriram
    BLOOD ADVANCES, 2017, 1 (23) : 2063 - 2074
  • [40] Altered glycosylation of platelet-derived von Willebrand factor confers resistance to ADAMTS13 proteolysis
    McGrath, Rachel T.
    van den Biggelaar, Maartje
    Byrne, Barry
    O'Sullivan, Jamie M.
    Rawley, Orla
    O'Kennedy, Richard
    Voorberg, Jan
    Preston, Roger J. S.
    O'Donnell, James S.
    BLOOD, 2013, 122 (25) : 4107 - 4110