Congenital Intestinal Lymphangiectasia: Report of a Case

被引：0

作者：

Hashemi, J. ^{[1
]}

Farhoodi, M. ^{[2
]}

Farrokh, D. ^{[1
]}

Pishva, A. ^{[1
]}

机构：

[1] Mashhad Univ Med Sci, Imam Reza Hosp, Dept Radiol, Mashhad, Iran

[2] Mashhad Univ Med Sci, Imam Reza Hosp, Dept Internal Med, Mashhad, Iran

来源：

IRANIAN JOURNAL OF RADIOLOGY | 2008年 / 5卷 / 04期

关键词：

Congenital; Intestinal Lymphangiectasis; Lymphatic System;

D O I：

暂无

中图分类号：

R8 [特种医学]; R445 [影像诊断学];

学科分类号：

1002 ; 100207 ; 1009 ;

摘要：

Congenital intestinal lymphangiectasia is a rare protein-losing enteropathy that usually affects children and young adults. Major symptoms include peripheral edema, mild non-bloody diarrhea, and chylous effusions that may develop during the course of the disease. In this disorder intestinal lymphatic vessels show fibrous occlusions that lead to pressure elevation of the lymphatic flow and rupture of the small lymphatic vessels. Transduction of lymph fluid into the different layers of the intestinal wall and lumen then occurs.

引用

页码：189 / 193

页数：5