Primary cerebral non-Langerhans cell histiocytosis: MRI and differential diagnosis

被引:32
作者
Ernemann, U
Skalej, M
Hermisson, M
Platten, M
Jaffe, R
Voigt, K
机构
[1] Univ Tubingen Hosp, Dept Neuroradiol, D-72076 Tubingen, Germany
[2] Univ Tubingen Hosp, Dept Neurol, D-72076 Tubingen, Germany
[3] Childrens Hosp Pittsburgh, Dept Pathol, Pittsburgh, PA 15213 USA
关键词
cerebral histiocytosis; non-Langerhans cell histiocytosis; juvenile xanthogranuloma; xanthoma disseminatum;
D O I
10.1007/s00234-002-0819-6
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We report a young woman with primary cerebral non-Langerhans cell histiocytosis of the juvenile xanthogranuloma family. The clinical course was complicated by extensive infiltration of cranial nerves and meninges and epi- and intramedullary spinal dissemination. Whereas the cutaneous form of juvenile xanthogranuloma is usually benign and self-limited, central nervous system involvement is associated with high morbidity and mortality and might therefore be considered a separate clinical entity.
引用
收藏
页码:759 / 763
页数:5
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