Primary hypertrophic osteoarthropathy (pachydermoperiostosis): a case report

被引:10
作者
Karkucak, Murat [1 ]
Erturk, Engin
Capkin, Erhan
Akyazi, Hikmet
Ozden, Gonca
Tosun, Mehmet
机构
[1] Karadeniz Tech Univ, Fac Med, Dept Phys Med & Rehabil, TR-61080 Trabzon, Turkey
[2] Karadeniz Tech Univ, Dept Anaesthesiol & Intens Care, TR-61080 Trabzon, Turkey
[3] Karadeniz Tech Univ, Dept Dermatol, Trabzon, Turkey
关键词
pachydermoperiostosis; primary hypertrophic osteoarthropathy; digital clubbing;
D O I
10.1007/s00296-006-0216-2
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Hypertrophic osteoarthropathy is characterized by digital clubbing and periosteal reaction of long bones. Most cases are associated with malignancy or other conditions such as congenital heart disease, liver cirrhosis, pulmonary fibrosis, biliary atresia, and gastrointestinal polyps. We report a 19-year-old man presenting with arthritis, broadening of the fingers and clubbing of the fingers and toes for the previous 3 years. The ankles and knees were swollen. X-rays showed periosteal apposition. The search for a secondary cause remained negative. In cases of arthralgia/arthritis together with clubbed fingers, consideration must be given to hypertrophic osteoarthropathy. The primary or idiopathic form is rare and has a good prognosis.
引用
收藏
页码:403 / 405
页数:3
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