Fatal bleeding following delivery:: A manifestation of the vascular type of Ehlers-Danlos' syndrome

被引：10
|
作者：
Bjorck, M. [1 ]
Pigg, M.
Kragsterman, B.
Bergqvist, D.
机构：
[1] Univ Uppsala Hosp, Dept Surg, Vasc Surg Sect, SE-75185 Uppsala, Sweden
[2] Univ Uppsala Hosp, Dept Genet & Pathol, Clin Genet Sect, SE-75185 Uppsala, Sweden
来源：
GYNECOLOGIC AND OBSTETRIC INVESTIGATION | 2007年 / 63卷 / 03期
关键词：
Ehlers-Danlos' syndrome; subclavian artery; delivery; bleeding; rupture;
D O I：
10.1159/000097659
中图分类号：
R71 [妇产科学];
学科分类号：
100211 ;
摘要：
Introduction: The vascular form of Ehlers-Danlos' syndrome (type IV) is a potentially lethal genetic condition because of rupture of major arteries, often in the peri-partum period. Case Report: We report a 31-year-old primipara who died from a rupture of the right subclavian artery. The patient had several symptoms and signs typical of the disease. The rupture occurred during the expulsion-phase of delivery but was recognized only on day 9. Conclusion: Early recognition is crucial to avoid maternal mortality due to this genetic disorder. Once the condition is suspected, the clinical diagnosis is straightforward. Copyright (c) 2007 S. Karger AG, Basel.
引用
收藏
页码：173 / 175
页数：3
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