Neonatal presentation of Caroli's disease

被引：18
作者：
Keane, F
Hadzic, N
Wilkinson, ML
Qureshi, S
Reid, C
Baker, AJ
MieliVergani, G
机构：
[1] UNIV LONDON KINGS COLL HOSP, DEPT CHILD HLTH, LONDON SE5 9RJ, ENGLAND
[2] GUYS HOSP, DEPT GASTROENTEROL, LONDON SE1 9RT, ENGLAND
[3] GUYS HOSP, DEPT PAEDIAT NEPHROL, LONDON SE1 9RT, ENGLAND
[4] GUYS HOSP, DEPT PAEDIAT CARDIOL, LONDON SE1 9RT, ENGLAND
来源：
ARCHIVES OF DISEASE IN CHILDHOOD-FETAL AND NEONATAL EDITION | 1997年 / 77卷 / 02期
关键词：
Caroli's disease; endoscopic retrograde cholangiopancreatography; pulmonary artery stenosis;
D O I：
10.1136/fn.77.2.F145
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
A neonatal presentation of Caroli's disease with severe cardiac and progressive renal pathology is described. The availability of small paediatric endoscopes ensured early diagnosis. Despite aggressive medical management, the baby died with severe bleeding complications before potentially life saving multiple organ transplantation could take place.
引用
收藏
页码：F145 / F146
页数：2
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