Right aortic arch with isolation of the left subclavian artery: a rare association with airway obstruction

被引:7
作者
Yubbu, Putri [1 ]
Latiff, Haifa A. [2 ]
Abbaker, Abdel Moneim Adam [3 ]
机构
[1] Univ Putra Malaysia, Fac Med & Hlth Sci, Dept Pediat, Serdang 43400, Selangor, Malaysia
[2] Natl Inst Hlth, Dept Paediat Cardiol, Kuala Lumpur, Malaysia
[3] Natl Inst Hlth, Cardiothorac Surg Dept, Kuala Lumpur, Malaysia
关键词
Isolated subclavian artery; pulmonary artery sling; airway obstruction; vascular ring; left bronchial isomerism; PULMONARY STEAL PHENOMENON; TETRALOGY; FALLOT;
D O I
10.1017/S1047951116001840
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We present two interesting cases of isolated left subclavian artery from the pulmonary artery with symptoms of upper airway obstruction. The first patient had tetralogy of Fallot, pulmonary artery sling, bilateral superior caval veins, and left bronchial isomerism, suggesting heterotaxy syndrome. The second patient had a right aortic arch, isolated left subclavian artery, and bilateral arterial ducts. These two cases are interesting because of their rarity and uncommon presentation.
引用
收藏
页码:613 / 616
页数:4
相关论文
共 10 条
[1]  
BRICKER JT, 1984, TEX HEART I J, V11, P84
[2]   Congenital pulmonary steal phenomenon associated with tetralogy of Fallot, right aortic arch, and isolation of the left subclavian artery [J].
Carano, N ;
Piazza, P ;
Agnetti, A ;
Squarcia, U .
PEDIATRIC CARDIOLOGY, 1997, 18 (01) :57-60
[3]  
EDWARDS JE, 1948, MED CLIN N AM, P925
[4]  
Filler R M, 1994, Semin Thorac Cardiovasc Surg, V6, P211
[5]   PULMONARY VASCULAR SLING - REPORT OF 7 CASES AND REVIEW OF THE LITERATURE [J].
GIKONYO, BM ;
JUE, KL ;
EDWARDS, JE .
PEDIATRIC CARDIOLOGY, 1989, 10 (02) :81-89
[6]  
LANDING BH, 1979, AM REV RESPIR DIS, V120, P151
[7]   Isolated right subclavian artery arising from the right pulmonary artery via a right-sided ductus arteriosus with associated pulmonary steal phenomenon [J].
Miller, Stephen G. ;
Campbell, Michael J. ;
Barker, Piers C. A. ;
Hill, Kevin D. .
CARDIOLOGY IN THE YOUNG, 2012, 22 (02) :216-218
[8]   22q11.2 Deletions in Patients with Conotruncal Defects: Data from 1,610 Consecutive Cases [J].
Peyvandi, Shabnam ;
Lupo, Philip J. ;
Garbarini, Jennifer ;
Woyciechowski, Stacy ;
Edman, Sharon ;
Emanuel, Beverly S. ;
Mitchell, Laura E. ;
Goldmuntz, Elizabeth .
PEDIATRIC CARDIOLOGY, 2013, 34 (07) :1687-1694
[9]  
SADE RM, 1975, J THORAC CARDIOV SUR, V69, P333
[10]   IMAGING STRATEGIES FOR VASCULAR RINGS [J].
VANSON, JAM ;
JULSRUD, PR ;
HAGLER, DJ ;
SIM, EKW ;
PUGA, FJ ;
SCHAFF, HV ;
DANIELSON, GK .
ANNALS OF THORACIC SURGERY, 1994, 57 (03) :604-610