Congenital absence of portal vein associated with nodular regenerative hyperplasia of the liver and pulmonary hypertension

被引：13

作者：

Peker, Ahmet ^{[1
]}

Ucar, Tayfun ^{[2
]}

Kuloglu, Zarife ^{[2
]}

Ceyhan, Koray ^{[3
]}

Tutar, Ercan ^{[2
]}

Fitoz, Suat ^{[1
]}

机构：

[1] Ankara Univ, Sch Med, Dept Radiol, TR-06100 Ankara, Turkey

[2] Ankara Univ, Sch Med, Dept Pediat, TR-06100 Ankara, Turkey

[3] Ankara Univ, Sch Med, Dept Pathol, TR-06100 Ankara, Turkey

来源：

CLINICAL IMAGING | 2009年 / 33卷 / 04期

关键词：

Portal vein; Congenital absence; Computed tomography; Ultrasonography; Magnetic resonance imaging; HEPATOPULMONARY SYNDROME;

D O I：

10.1016/j.clinimag.2008.12.011

中图分类号：

R8 [特种医学]; R445 [影像诊断学];

学科分类号：

1002 ; 100207 ; 1009 ;

摘要：

We present a 15-year-old girl with congenital absence of the portal vein, pulmonary arterial hypertension and multiple liver lesions proven to be nodular regenerative hyperplasia with biopsy. Ultrasonography, computed tomography, and magnetic resonance imaging findings of the liver lesions and Type I portosystemic shunt are presented. (C) 2009 Elsevier Inc. All rights reserved.

引用

页码：322 / 325

页数：4

共 17 条

[1] Abernethy malformation: One of the etiologies of hepatopulmonary syndrome [J].

Alvarez, AE ;

Ribeiro, AF ;

Hessel, G ;

Baracat, J ;

Ribeiro, JD .

PEDIATRIC PULMONOLOGY, 2002, 34 (05) :391-394

[2] Portal vein absence and nodular regenerative hyperplasia of the liver with giant inferior mesenteric vein [J].

Arana, E ;

MartiBonmati, L ;

Martinez, V ;

Hoyos, M ;

Montes, H .

ABDOMINAL IMAGING, 1997, 22 (05) :506-508

[3] Pseudotumoral presentation of nodular regenerative hyperplasia of the liver: Imaging in five patients including MR imaging [J].

Casillas, C ;

MartiBonmati, L ;

Galant, J .

EUROPEAN RADIOLOGY, 1997, 7 (05) :654-658

[4] Congenital absence of portal vein presenting as hepatopulmonary syndrome [J].

Cheung, KM ;

Lee, CY ;

Wong, CT ;

Chan, AKH .

JOURNAL OF PAEDIATRICS AND CHILD HEALTH, 2005, 41 (1-2) :72-75

[5] An infant with pulmonary hypertension due to a congenital porto-caval shunt [J].

Ersch, N ;

Bänziger, O ;

Braegger, C ;

Arbenz, U ;

Stallmach, T .

EUROPEAN JOURNAL OF PEDIATRICS, 2002, 161 (12) :660-662

[6] Congenital absence of portal vein with nodular regenerative hyperplasia of the liver [J].

Grazioli, L ;

Alberti, D ;

Olivetti, L ;

Rigamonti, W ;

Codazzi, F ;

Matricardi, L ;

Fugazzola, C ;

Chiesa, A .

EUROPEAN RADIOLOGY, 2000, 10 (05) :820-825

[7] PULMONARY-HYPERTENSION COMPLICATING PORTAL-HYPERTENSION - PREVALENCE AND RELATION TO SPLANCHNIC HEMODYNAMICS [J].

HADENGUE, A ;

BENHAYOUN, MK ;

LEBREC, D ;

BENHAMOU, JP .

GASTROENTEROLOGY, 1991, 100 (02) :520-528

[8] Pulmonary hypertension as a result of asymptomatic portosystemic shunt [J].

Imamura, H ;

Momose, T ;

Kitabayashi, H ;

Takahashi, W ;

Yazaki, Y ;

Takenaka, H ;

Isobe, M ;

Sekiguchi, M ;

Kubo, K .

JAPANESE CIRCULATION JOURNAL-ENGLISH EDITION, 2000, 64 (06) :471-473

[9] Congenital absence of the portal vein associated with focal nodular hyperplasia of the liver and congenital choledochal cyst: A case report [J].

Kinjo, T ;

Aoki, H ;

Sunagawa, H ;

Kinjo, S ;

Muto, Y .

JOURNAL OF PEDIATRIC SURGERY, 2001, 36 (04) :622-625

[10] Benign nodular hepatocellular lesions caused by abnormal hepatic circulation: Etiological analysis and introduction of a new concept [J].

Kondo, F .

JOURNAL OF GASTROENTEROLOGY AND HEPATOLOGY, 2001, 16 (12) :1319-1328

← 1 2 →