Extranodal NK/T-cell lymphoma, nasal type

被引:79
作者
Al-Hakeem, Data Abdullah
Fedele, Stefano
Carlos, Roman
Porter, Stephen
机构
[1] UCL, Eastman Dent Inst Oral Hlth Care Sci, Oral Med Unit, Div Maxillofacial Diagnost Med & Surg Sci, London WC1X 8LD, England
[2] Ctr Med Oral Guatemala, Guatemala City 01010, Guatemala
关键词
lymphoma; nasal lymphoma; oral lymphoma; NK/T-cell;
D O I
10.1016/j.oraloncology.2006.03.011
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
Extranodal NK/T-cell lymphoma, nasal type (ENKTCL), previously known as lethal midline granuloma is a distinct clinico-pathological entity associated with Epstein-Barr virus that typically causes destruction of the midface, palatal and orbital-walls. In addition, ENKTCL can involve the skin, soft tissue, testes, gastrointestinal and upper respiratory tract. ENKTCL neoplastic cells express some T-cell associated antigens, most commonly CD2 and cytoplasmic CD3 epsilon and, in favour of an NK-cell origin, CD56. Early stage disease may respond to radiotherapy alone, however late stage disease does not respond well to any available therapies. Overall, patients with ENKTCL have a cumulative probability of survival at 5 years ranging from 37.9% to 45.3%. (c) 2006 Elsevier Ltd. All rights reserved.
引用
收藏
页码:4 / 14
页数:11
相关论文
共 155 条
[1]   Nasal and nasal type CD56+natural killer cell/T-cell lymphoma: a case with rapid progression to bone marrow involvement [J].
Ahn, SJ ;
Jang, KA ;
Choi, JH ;
Sung, KJ ;
Moon, KC ;
Koh, JK .
BRITISH JOURNAL OF DERMATOLOGY, 2000, 142 (05) :1021-1025
[2]   INVOLVEMENT OF INTERFERON-GAMMA AND MACROPHAGE-COLONY-STIMULATING FACTOR IN PATHOGENESIS OF HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS IN ADULTS [J].
AKASHI, K ;
HAYASHI, S ;
GONDO, H ;
MIZUNO, S ;
HARADA, M ;
TAMURA, K ;
YAMASAKI, K ;
SHIBUYA, T ;
UIKE, N ;
OKAMURA, T ;
MIYAMOTO, T ;
NIHO, Y .
BRITISH JOURNAL OF HAEMATOLOGY, 1994, 87 (02) :243-250
[3]  
Altemani A, 2002, NEOPLASMA, V49, P55
[4]   CD56-positive (nasal-type T NK cell) lymphoma arising on the skin - Report of two cases and review of the literature [J].
Ansai, S ;
Maeda, K ;
Yamakawa, M ;
Matsuda, M ;
Saitoh, S ;
Suwa, S ;
Saitoh, H ;
Ohtsuka, M ;
Iwatsuki, K .
JOURNAL OF CUTANEOUS PATHOLOGY, 1997, 24 (08) :468-476
[5]   LETHAL MIDLINE GRANULOMA IN SEOUL (KOREA) AND SHANGHAI (CHINA) [J].
AOZASA, K ;
YANG, WI ;
LEE, YB ;
PAN, WS ;
WU, YF ;
HORIUCHI, K ;
HYUN, BH ;
TAJIMA, K .
INTERNATIONAL JOURNAL OF CANCER, 1992, 52 (04) :673-674
[6]   NON-HODGKIN LYMPHOMAS IN OSAKA, JAPAN [J].
AOZASA, K ;
TSUJIMOTO, M ;
SAKURAI, M ;
HONDA, M ;
YAMASHITA, K ;
HANADA, M ;
SUGIMOTO, A .
EUROPEAN JOURNAL OF CANCER & CLINICAL ONCOLOGY, 1985, 21 (04) :487-&
[7]   NASAL LYMPHOMAS IN PERU - HIGH-INCIDENCE OF T-CELL IMMUNOPHENOTYPE AND EPSTEIN-BARR-VIRUS INFECTION [J].
ARBER, DA ;
WEISS, LM ;
ALBUJAR, PF ;
CHEN, YY ;
JAFFE, ES .
AMERICAN JOURNAL OF SURGICAL PATHOLOGY, 1993, 17 (04) :392-399
[8]   Mosquito salivary gland extracts induce EBV-infected NK cell oncogenesis via CD4+T cells in patients with hypersensitivity to mosquito bites [J].
Asada, H ;
Saito-Katsuragi, M ;
Niizeki, H ;
Yoshioka, A ;
Suguri, S ;
Isonokami, M ;
Aoki, T ;
Ishihara, S ;
Tokura, Y ;
Iwatsuki, K ;
Miyagawa, S .
JOURNAL OF INVESTIGATIVE DERMATOLOGY, 2005, 125 (05) :956-961
[9]   Quantification of circulating Epstein-Barr virus (EBV) DNA in the diagnosis and monitoring of natural killer cell and EBV-positive lymphomas in immunocompetent patients [J].
Au, WY ;
Pang, A ;
Choy, C ;
Chim, CS ;
Kwong, YL .
BLOOD, 2004, 104 (01) :243-249
[10]   Testicular natural killer T-cell lymphoma [J].
Ballereau, C ;
Leroy, X ;
Morschhauser, F ;
Fantoni, JC ;
Lemaitre, L ;
Villers, A ;
Biserte, J .
INTERNATIONAL JOURNAL OF UROLOGY, 2005, 12 (02) :223-224