Dark-Rearing the rd10 Mouse: Implications for Therapy

被引:22
作者
Cronin, Therese [1 ]
Lyubarsky, Arkady [1 ]
Bennett, Jean [1 ]
机构
[1] Univ Penn, FM Kirby Ctr Mol Ophthalmol, Philadelphia, PA 19104 USA
来源
RETINAL DEGENERATIVE DISEASES | 2012年 / 723卷
关键词
Dark-rearing; Phosphodiesterase; 6b; rd10 Mouse model; Rod ON-bipolar cells; Electroretinogram; ROD CGMP-PHOSPHODIESTERASE; RETINAL DEGENERATION; RETINITIS-PIGMENTOSA; BETA-SUBUNIT; LIGHT; MODEL; RHODOPSIN; GENE; RATS; MICE;
D O I
10.1007/978-1-4614-0631-0_18
中图分类号
Q [生物科学];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:129 / 136
页数:8
相关论文
共 20 条
[1]  
Bicknell IR, 2002, MOL VIS, V8, P333
[2]   RETINAL DEGENERATION IN THE RD MOUSE IS CAUSED BY A DEFECT IN THE BETA-SUBUNIT OF ROD CGMP-PHOSPHODIESTERASE [J].
BOWES, C ;
LI, TS ;
DANCIGER, M ;
BAXTER, LC ;
APPLEBURY, ML ;
FARBER, DB .
NATURE, 1990, 347 (6294) :677-680
[3]   Two mouse retinal degenerations caused by missense mutations in the β-subunit of rod cGMP phosphodiesterase gene [J].
Chang, B. ;
Hawes, N. L. ;
Pardue, M. T. ;
German, A. M. ;
Hurd, R. E. ;
Davisson, M. T. ;
Nusinowitz, S. ;
Rengarajan, K. ;
Boyd, A. P. ;
Sidney, S. S. ;
Phillips, M. J. ;
Stewart, R. E. ;
Chaudhury, R. ;
Nickerson, J. M. ;
Heckenlively, J. R. ;
Boatright, J. H. .
VISION RESEARCH, 2007, 47 (05) :624-633
[4]   Retinal degeneration mutants in the mouse [J].
Chang, B ;
Hawes, NL ;
Hurd, RE ;
Davisson, MT ;
Nusinowitz, S ;
Heckenlively, JR .
VISION RESEARCH, 2002, 42 (04) :517-525
[5]   Functional Remodeling of Glutamate Receptors by Inner Retinal Neurons Occurs From an Early Stage of Retinal Degeneration [J].
Chua, Jacqueline ;
Fletcher, Erica L. ;
Kalloniatis, Michael .
JOURNAL OF COMPARATIVE NEUROLOGY, 2009, 514 (05) :473-491
[6]   In vivo dynamics of retinal injury and repair in the rhodopsin mutant dog model of human retinitis pigmentosa [J].
Cideciyan, AV ;
Jacobson, SG ;
Aleman, TS ;
Gu, DN ;
Pearce-Kelling, SE ;
Sumaroka, A ;
Acland, GM ;
Aguirre, GD .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 2005, 102 (14) :5233-5238
[7]   INHERITED RETINAL DYSTROPHY IN RAT [J].
DOWLING, JE ;
SIDMAN, RL .
JOURNAL OF CELL BIOLOGY, 1962, 14 (01) :73-+
[8]   Retinal organization in the retinal degeneration 10 (rd10) mutant mouse: A morphological and ERG study [J].
Gargini, Claudia ;
Terzibasi, Eva ;
Mazzoni, Francesca ;
Strettoi, Enrica .
JOURNAL OF COMPARATIVE NEUROLOGY, 2007, 500 (02) :222-238
[9]   RETINAL DEGENERATION IN RCS RATS RAISED UNDER AMBIENT LIGHT LEVELS [J].
KAITZ, M ;
AUERBACH, E .
VISION RESEARCH, 1979, 19 (01) :79-81
[10]   Functionally rodless mice: transgenic models for the investigation of cone function in retinal disease and therapy [J].
Lyubarsky, AL ;
Lem, J ;
Chen, J ;
Falsini, B ;
Iannaccone, A ;
Pugh, EN .
VISION RESEARCH, 2002, 42 (04) :401-415