Moebius syndrome and central respiratory dysfunction

被引:19
作者
Igarashi, M
Rose, DF
Storgion, SA
机构
[1] UNIV TENNESSEE,DEPT PEDIAT,NEUROL SECT,MEMPHIS,TN
[2] UNIV TENNESSEE,DEPT PEDIAT,SECT CRIT CARE MED,MEMPHIS,TN
[3] LEBONHEUR CHILDRENS HOSP & MED CTR,MEMPHIS,TN
关键词
D O I
10.1016/S0887-8994(97)00012-X
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Two infants, 18 months and 4 months of age, who were born with bilateral VI and VII nerve palsy (Moebius syndrome) experienced central respiratory failure requiring persistent ventilation. The computed tomography scan showed small brainstem tegmental calcifications. These findings suggest intrauterine brainstem necrosis including the respiratory center and poor prognosis for independent respiration. (C) 1997 by Elsevier Science Inc.
引用
收藏
页码:237 / 240
页数:4
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