Liver imaging findings of Wilson's disease

被引:22
作者
Akpinar, Erhan [1 ]
Akhan, Okan [1 ]
机构
[1] Hacettepe Univ, Fac Med, Dept Radiol, TR-06100 Ankara, Turkey
关键词
Wilson's disease; liver; ultrasound; CT; MRI;
D O I
10.1016/j.ejrad.2006.11.006
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
Wilson's disease is a rare, autosomal-recessive inherited disorder of copper metabolism resulting in accumulation of copper in liver. The form of liver disease varies, depending on the severity of the disease at the time of diagnosis and pathological findings include fatty changes, acute hepatitis, chronic active hepatitis, cirrhosis and occasionally fulminant hepatic necrosis. Liver imaging findings reflect a wide range of physiopathological processes of the disease and also demonstrate the associated findings of cirrhosis in cases with advanced disease. (C) 2006 Elsevier Ireland Ltd. All rights reserved.
引用
收藏
页码:25 / 32
页数:8
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