An approach to the diagnosis and treatment of cryofibrinogenemia

被引:59
作者
Amdo, TD [1 ]
Welker, JA [1 ]
机构
[1] Harbor Hosp Ctr, Dept Internal Med, Hospitalist Sect, Baltimore, MD 21225 USA
关键词
D O I
10.1016/j.amjmed.2003.09.033
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Cryofibrinogenemia is a rarely symptomatic disorder that is underrecognized due to the infrequency with which it causes symptoms. Although completely reversible, this disorder can be life threatening when untreated. In this review, the classification, pathophysiology, and clinical presentation of cryofibrinogenemia are described, based on case reports and prospective observational data. Diagnostic criteria are outlined, and therapies are assessed critically. This information should help clinicians in establishing a diagnosis of cryofibrinogenemia and initiating treatment. (C) 2004 by Excerpta Medica Inc.
引用
收藏
页码:332 / 337
页数:6
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