Use of daytime phototherapy for Crigler-Najjar disease

被引：6

作者：

Nydegger, A

Bednarz, A

Hardikar, W

机构：

[1] Royal Childrens Hosp, Dept Gastroenterol & Nutr, Melbourne, Vic, Australia

[2] Royal Childrens Hosp, Dept Biomed Engn, Melbourne, Vic, Australia

来源：

JOURNAL OF PAEDIATRICS AND CHILD HEALTH | 2005年 / 41卷 / 07期

关键词：

Crigler-Najjar syndrome; glucuronyltransferase; hereditary; hyperbilirubinemia; phototherapy;

D O I：

10.1111/j.1440-1754.2005.00642.x

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Crigler-Najjar syndrome type 1 (CNS1) is characterized by a severe unconjugated hyperbilirubinemia from birth. Intensive blue-light phototherapy is the standard method for management; however, it imposes severe restrictions on the child and their family's lifestyle. We describe here the use of a novel sit-up phototherapy unit in a child with CNS1. The unit allowed a 50% reduction in phototherapy time while maintaining efficacy, thus enabling the child to attend school.

引用

页码：387 / 389

页数：3

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