Primary Cutaneous Composite Lymphomas

被引:6
作者
Chen, Stephanie [1 ]
Boyer, Daniel [2 ]
Hristov, Alexandra C. [2 ,3 ]
机构
[1] Univ Iowa Hlth Care, Dept Pathol, Iowa City, IA USA
[2] Univ Michigan, Med Ctr, Dept Pathol, Ann Arbor, MI 48109 USA
[3] Univ Michigan, Med Ctr, Dept Dermatol, Ann Arbor, MI 48109 USA
关键词
B-CELL LYMPHOMA; T-CELL; MYCOSIS-FUNGOIDES; HODGKINS-DISEASE; FOLLICULAR LYMPHOMA; CLINICOPATHOLOGICAL ANALYSIS; LYMPHOCYTIC-LEUKEMIA; BICLONAL LYMPHOMAS; MANTLE CELL; PATIENT;
D O I
10.5858/arpa.2018-0283-RA
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
摘要
Composite lymphomas have been defined as 2 distinct subtypes of lymphoma occurring at a single anatomic site. Composite lymphomas limited to the skin are a rare occurrence and pose a unique challenge. Many reported cases within the skin are combined B-cell and T-cell lymphomas, typically mycosis fungoides and a low-grade B-cell lymphoma. These cases are challenging to recognize because lymphoid infiltrates within the skin often include a mixed population of B cells and T cells. In particular, reactive lymphoid proliferations (pseudolymphomas), primary cutaneous low-grade B-cell lymphomas, and primary cutaneous CD4+ T-cell lymphoproliferative disorder may show nearly equal numbers of B cells and T cells. In order to exclude these possibilities, overwhelming evidence in support of each lymphoma is helpful, including abnormal architecture, cytology, and immunophenotype, as well as molecular genetic evidence of clonality.
引用
收藏
页码:1352 / 1357
页数:6
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