Symptomatic myocardial bridges in children: a case report with review of literature

被引:13
作者
Sharma, Jayendra [1 ]
Hellenbrand, William [1 ]
Kleinman, Charles [1 ]
Mosca, Ralph [2 ]
机构
[1] Columbia Univ, Div Pediat Cardiol, New York, NY 10032 USA
[2] Columbia Univ, Dept Pediat, Morgan Stanley Childrens Hosp, New York Presbyterian Med Ctr, New York, NY 10032 USA
关键词
Hypertrophic cardiomyopathy; coronary ischaemia; supra-arterial myotomy; sudden cardiac death; HYPERTROPHIC CARDIOMYOPATHY; CORONARY-ARTERY; MYOTOMY;
D O I
10.1017/S1047951111000849
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Myocardial bridge is a rare congenital coronary anomaly in children, usually seen in the setting of hypertrophic cardiomyopathy and in left ventricular hypertrophy. Most myocardial bridges are believed to represent a benign anatomical variant; however, symptomatic myocardial bridge is a distinct subgroup of pathological variant, linked to myocardial ischaemia, ventricular arrhythmia, and sudden cardiac death. We present a case of a symptomatic myocardial bridge in a 5-year-old boy with mild hypertrophic cardiomyopathy who underwent supra-arterial myotomy, automatic defibrillator placement, and long-term Beta-blocker therapy. We also present 10 years of follow-up with a review of literature regarding symptomatic myocardial bridges in the paediatric age group.
引用
收藏
页码:490 / 494
页数:5
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