Erdheim-Chester's disease of the heart:: A diagnostic conundrum and collision with the same mass in the orbit

被引:3
作者
Bogáts, G
Piros, G
Tiszlavicz, L
Iványi, B
Sasi, V
Csepregil, L
Simon, J
Babik, B
Csillik, A
Kardos, L
Palkó, A
Matin, K
Hanzély, Z
Korányi, K
Nyáry, I
Végh, M
Kolozsvári, L
Kahán, Z
Bajcsay, A
Tóth, A
Balázs, G
Simor, T
Pávics, L
Palotás, A
机构
[1] Univ Szeged, Div Cardiac Surg, Ctr Cardiol, H-6720 Szeged, Hungary
[2] Univ Szeged, Fac Med, Albert Szent Gyorgyi Med & Pharmaceut Ctr, Dept Psychiat, H-6720 Szeged, Hungary
[3] Univ Szeged, Fac Med, Albert Szent Gyorgyi Med & Pharmaceut Ctr, Dept Nucl Med, H-6720 Szeged, Hungary
[4] Univ Szeged, Fac Med, Albert Szent Gyorgyi Med & Pharmaceut Ctr, Dept Oncotherapy, H-6720 Szeged, Hungary
[5] Univ Szeged, Fac Med, Albert Szent Gyorgyi Med & Pharmaceut Ctr, Dept Ophthalmol, H-6720 Szeged, Hungary
[6] Univ Szeged, Fac Med, Albert Szent Gyorgyi Med & Pharmaceut Ctr, Dept Radiol, H-6720 Szeged, Hungary
[7] Univ Szeged, Fac Med, Albert Szent Gyorgyi Med & Pharmaceut Ctr, Dept Anesthesiol & Intens Therapy, H-6720 Szeged, Hungary
[8] Univ Szeged, Fac Med, Albert Szent Gyorgyi Med & Pharmaceut Ctr, Dept Pathol, H-6720 Szeged, Hungary
[9] Szeged Municipal Hosp, Dept Med, Szeged, Hungary
[10] Int Med Ctr, Szeged, Hungary
[11] Natl Inst Neurosurg & Res, Dept Neuropathol, Budapest, Hungary
[12] Natl Inst Neurosurg & Res, Dept Neuroophthalmol, Budapest, Hungary
[13] Natl Inst Neurosurg & Res, Dept Neurosurg, Budapest, Hungary
[14] Natl Inst Oncol, Dept Radiotherapy, Budapest, Hungary
[15] Semmelweis Univ, Div Radiol, Vasc & Cardiac Surg Dept, H-1085 Budapest, Hungary
[16] Univ Pecs, Fac Med, Dept Cardiol, Pecs, Hungary
关键词
D O I
10.1532/HSF98.20051109
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Erdheim-Chester's disease is a rare multisystem xanthogranulomatosis, afflicting the skeletal system with the occasional involvement of soft tissues. We delineate an unusual case of a cardiac variant of Erdheim-Chester's disease presenting with pericardial effusion and as a collision with a synchronous orbital manifestation. We describe our diagnostic pathway and propose a novel treatment option involving nonsteroidal anti-inflammatory drugs. The role of cyclo-oxygenase in the disease process and inhibition thereof by NSAIDs is hypothesized and discussed.
引用
收藏
页码:E549 / E554
页数:6
相关论文
共 8 条
[1]   The lipogranulomatosis. [J].
Chester, W .
VIRCHOWS ARCHIV FUR PATHOLOGISCHE ANATOMIE UND PHYSIOLOGIE UND FUR KLINISCHE MEDIZIN, 1930, 279 (02) :561-602
[2]  
CLINE MJ, 1994, BLOOD, V84, P2840
[3]   Cardiovascular involvement, an overlooked feature of Erdheim-Chester disease -: Report of 6 new cases and a literature review [J].
Haroche, J ;
Amoura, Z ;
Dion, E ;
Wechsler, B ;
Costedoat-Chalumeau, N ;
Cacoub, P ;
Isnard, R ;
Généreau, T ;
Wechsler, J ;
Weber, N ;
Graef, C ;
Cluzel, P ;
Grenier, P ;
Piette, JC .
MEDICINE, 2004, 83 (06) :371-392
[4]   Erdheim-Chester disease:: a case report and literature overview [J].
Kenn, W ;
Stäbler, A ;
Zachoval, R ;
Zietz, C ;
Raum, W ;
Wittenberg, G .
EUROPEAN RADIOLOGY, 1999, 9 (01) :153-158
[5]   Erdheim-Chester disease of the jaws: Literature review and case report [J].
Petrikowski, CG ;
McGaw, WT .
ORAL SURGERY ORAL MEDICINE ORAL PATHOLOGY ORAL RADIOLOGY AND ENDODONTOLOGY, 2000, 90 (03) :389-398
[6]  
SERRATRICE J, J RHEUMATOL, V27, P1550
[7]   The role of cyclooxygenase inhibition in the antineoplastic effects of nonsteroidal antiinflammatory drugs (NSAIDs) [J].
Shiff, SJ ;
Rigas, B .
JOURNAL OF EXPERIMENTAL MEDICINE, 1999, 190 (04) :445-450
[8]   Erdheim-Chester disease - Clinical and radiologic characteristics of 59 cases [J].
VeyssierBelot, C ;
Cacoub, P ;
CaparrosLefebvre, D ;
Wechsler, J ;
Brun, B ;
Remy, M ;
Wallaert, B ;
Petit, H ;
Grimaldi, A ;
Wechsler, B ;
Godeau, P .
MEDICINE, 1996, 75 (03) :157-169