Treatment of a life-threatening acute chest syndrome with hemolytic crisis in sickle cell disease using an extracorporeal membrane oxygenation (ECMO)

被引：8

作者：

Hoffmann, M. ^{[1
]}

Geldner, G. ^{[1
]}

Leschke, M.

机构：

[1] Klinikum Ludwigsburg, Klin Anasthesie Intens Med Schmerztherapie & Notf, D-71640 Ludwigsburg, Germany

来源：

DEUTSCHE MEDIZINISCHE WOCHENSCHRIFT | 2011年 / 136卷 / 43期

关键词：

severe sickle cell disease; acute chest syndrome; lung failure; ECMO (extracorporeal membrane oxygenation); NITRIC-OXIDE; ANEMIA; TRANSFUSIONS; GERMANY; STROKE;

D O I：

10.1055/s-0031-1292031

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

History and clinical findings: A 28-year-old male patient with sickle cell disease developed a vasoocclusive crisis with an acute chest syndrome and severe lung failure. Treatment and course: After partial substitution transfusion the patient was successfully treated extracorporeal membrane oxygenation (ECMO). After 12 days he was weaned from the ECMO, 2 days later the patient's tracheostoma was removed. 19 days after the event the patient had recovered completely and was moved to a hospital in Paris from where he came. Conclusion: Apparently data is sparse regarding the use of ECMO for treatment of a life-threatening acute chest syndrome in sickle cell disease. However, the therapy approach seems to be promising and is worth considering in this particular situation.

引用

页码：2192 / 2195

页数：4

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