Erythromelalgia: A pathognomonic microvascular thrombotic complication in essential thrombocythemia and polycythemia vera

被引:59
作者
Van Genderen, PJJ
Michiels, JJ
机构
[1] Goodheart Inst, Thrombocythemia Vera Study Grp, NL-3069 AT Rotterdam, Netherlands
[2] Erasme Univ Hosp, Dept Internal Med & Hematol 2, Rotterdam, Netherlands
关键词
erythromelalgia; essential thrombocythemia; polycythemia vera; myeloproliferative disorders; thrombosis;
D O I
10.1055/s-2007-996109
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Erythromelalgia is a characteristic thrombotic complication in patients with the myeloproliferative disorders, essential thrombocythemia and polycythemia vera. In this minireview, which is based on mort, than 20 years of clinical observations and intervention studies, the clinical manifestations, treatment, and pathogenesis of erythromelalgia are discussed.
引用
收藏
页码:357 / 363
页数:7
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