Skeletal fragility: an emerging complication of Ehlers-Danlos syndrome

被引：13

作者：

Formenti, Anna Maria ^{[1
]}

Doga, Mauro ^{[2
]}

Frara, Stefano ^{[2
]}

Ritelli, Marco ^{[3
]}

Colombi, Marina ^{[3
]}

Banfi, Giuseppe ^{[1
,2
]}

Giustina, Andrea ^{[2
]}

机构：

[1] Ist Ortoped Galeazzi, IRCCS, Milan, Italy

[2] Univ Vita Salute San Raffaele, Milan, Italy

[3] Univ Brescia, Dept Mol & Translat Med, Brescia, Italy

来源：

ENDOCRINE | 2019年 / 63卷 / 02期

关键词：

Osteoporosis; Vertebral fractures; Ehlers-Danlos syndrome; Bone mineral density; Bone structure; RADIOLOGICAL VERTEBRAL FRACTURES; JOINT HYPERMOBILITY; ADULT PATIENTS; OSTEOGENESIS IMPERFECTA; HIGH PREVALENCE; BONE; OSTEOPOROSIS; CLASSIFICATION; DIAGNOSIS; CHILDREN;

D O I：

10.1007/s12020-018-1822-y

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Ehlers-Danlos syndrome (EDS) is an emerging cause of skeletal fragility. Mechanism of bone damage are probably multifactorial in line with the different skeletal phenotypes that can be found in clinical practice. A structured approach to clinical management of bone metabolic complication in EDS is proposed.

引用

页码：225 / 230

页数：6

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