Mechanisms of disease - Folding of secretory and membrane proteins

被引:106
作者
Kuznetsov, G
Nigam, SK
机构
[1] Harvard Univ, Sch Med, Inst Med, Boston, MA 02115 USA
[2] Brigham & Womens Hosp, Dept Med, Div Renal, Boston, MA 02115 USA
[3] Eisai Res Inst, Andover, MA USA
关键词
D O I
10.1056/NEJM199812033392307
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
[No abstract available]
引用
收藏
页码:1688 / 1695
页数:8
相关论文
共 71 条
[1]   CELL-TYPE-SPECIFIC ADHESIVE INTERACTIONS OF SKELETAL MYOBLASTS WITH THROMBOSPONDIN-1 [J].
ADAMS, JC ;
LAWLER, J .
MOLECULAR BIOLOGY OF THE CELL, 1994, 5 (04) :423-437
[2]  
Anfinsen C B, 1975, Adv Protein Chem, V29, P205, DOI 10.1016/S0065-3233(08)60413-1
[3]   MISSENSE MUTATIONS IMPAIR INTRACELLULAR PROCESSING OF FIBRILLIN AND MICROFIBRIL ASSEMBLY IN MARFAN-SYNDROME [J].
AOYAMA, T ;
TYNAN, K ;
DIETZ, HC ;
FRANCKE, U ;
FURTHMAYR, H .
HUMAN MOLECULAR GENETICS, 1993, 2 (12) :2135-2140
[4]   A Thr(359)Met mutation in factor VII of a patient with a hereditary deficiency causes defective secretion of the molecule [J].
Arbini, AA ;
Mannucci, PM ;
Bauer, KA .
BLOOD, 1996, 87 (12) :5085-5094
[5]   CALNEXIN - A MEMBRANE-BOUND CHAPERONE OF THE ENDOPLASMIC-RETICULUM [J].
BERGERON, JJM ;
BRENNER, MB ;
THOMAS, DY ;
WILLIAMS, DB .
TRENDS IN BIOCHEMICAL SCIENCES, 1994, 19 (03) :124-128
[6]  
BLANK CA, 1994, ANN ALLERGY, V72, P305
[7]   AFFINITY PANNING OF A LIBRARY OF PEPTIDES DISPLAYED ON BACTERIOPHAGES REVEALS THE BINDING-SPECIFICITY OF BIP [J].
BLONDELGUINDI, S ;
CWIRLA, SE ;
DOWER, WJ ;
LIPSHUTZ, RJ ;
SPRANG, SR ;
SAMBROOK, JF ;
GETHING, MJH .
CELL, 1993, 75 (04) :717-728
[8]   INDUCTION OF THE FK506-BINDING PROTEIN, FKBP13, UNDER CONDITIONS WHICH MISFOLD PROTEINS IN THE ENDOPLASMIC-RETICULUM [J].
BUSH, KT ;
HENDRICKSON, BA ;
NIGAM, SK .
BIOCHEMICAL JOURNAL, 1994, 303 :705-708
[9]  
BUSH KT, 1995, BIOCHEM J, V305, P1031
[10]  
Bush KT, 1997, J BIOL CHEM, V272, P9086