Female form persistent mullerian duct syndrome: MDCT findings

被引:15
作者
Clemente, Alberto [2 ]
Macchi, Veronica [3 ]
Berretta, Massimiliano [4 ]
Morra, Aldo [1 ]
机构
[1] Euganea Med Diagnost Ctr, Dept Radiol, I-35020 Padua, Italy
[2] Univ Ferrara, Dept Radiol, I-44100 Ferrara, Italy
[3] Univ Padua, Dept Human Anat & Physiol, Sect Anat, I-35100 Padua, Italy
[4] Natl Canc Inst, Div Med Oncol, Aviano, Italy
关键词
genitourinary system; abnormalities; testis; undescended; CT; spiral; computer applications; 3D;
D O I
10.1016/j.clinimag.2007.11.002
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
Persistent mullerian duct syndrome (PMDS) is a rare form of male pseudohermaphroditism. Two anatomic forms are described in this syndrome, the male and the female one; the second one is usually associated with bilateral cryptorchidism. About 150 cases are reported in literature; most of them are focused on anatomical, genetic, and surgical aspects. Radiological imaging features, important for diagnosis and therapy planification, are rarely reported. We describe a case of a female type of PMDS studied with multidetector computed tomography. (c) 2008 Elsevier Inc. All rights reserved.
引用
收藏
页码:314 / 317
页数:4
相关论文
共 20 条
[1]   RADIOLOGICAL FINDINGS IN 3 CASES OF PERSISTENT MULLERIAN DUCT SYNDROME [J].
ADAMSBAUM, C ;
ROLLAND, Y ;
JOSSO, N ;
KALIFA, G .
PEDIATRIC RADIOLOGY, 1993, 23 (01) :55-56
[2]  
[Anonymous], 1939, ACTA CHIR SCAND
[3]  
Belville C, 1999, AM J MED GENET, V89, P218, DOI 10.1002/(SICI)1096-8628(19991229)89:4<218::AID-AJMG6>3.0.CO
[4]  
2-E
[5]   Persistent Mullerian duct syndrome with or without transverse testicular ectopia and testis tumours [J].
Berkmen, F .
BRITISH JOURNAL OF UROLOGY, 1997, 79 (01) :122-126
[6]  
Berkmen F, 1998, J EXP CLIN CANC RES, V17, P409
[7]   PERSISTENT MULLERIAN DUCT SYNDROME - REPORTS OF 2 CASES [J].
BEYRIBEY, S ;
CETINKAYA, M ;
ADSAN, O ;
MEMIS, A ;
OZTURK, B .
SCANDINAVIAN JOURNAL OF UROLOGY AND NEPHROLOGY, 1993, 27 (04) :563-565
[8]   Persistent Mullerian duct syndrome [J].
Dekker, HM ;
de Jong, IJ ;
Sanders, J ;
Wolf, RFE .
RADIOGRAPHICS, 2003, 23 (02) :309-313
[9]   US and MRI in a case of persistent Mullerian duct syndrome [J].
Di Cesare, E ;
De Vincentiis, VD ;
Maffey, MV ;
Splendiani, A ;
Masciocchi, C .
PEDIATRIC RADIOLOGY, 1998, 28 (11) :865-867
[10]  
GUERRIER D, 1989, J CLIN ENDOCR METAB, V68, P48