Pulmonary alveolar proteinosis and end-stage pulmonary fibrosis - A rare association

被引:16
作者
Agarwal, PP
Seely, JM
Perkins, DG
Matzinger, FR
Alikhan, Q
机构
[1] Ottawa Hosp, Dept Diagnost Imaging, Ottawa, ON K1Y 4E9, Canada
[2] Ottawa Hosp, Dept Lab Med, Div Anat Pathol, Ottawa, ON K1Y 4E9, Canada
[3] Ottawa Hosp, Div Rehabil Med Pulm, Ottawa, ON K1Y 4E9, Canada
关键词
pulmonary alveolar proteinosis; high resolution CT; fibrosis;
D O I
10.1097/01.rti.0000160733.74997.2d
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
We present the high resolution CT features of marked pulmonary fibrosis in a patient known to have pulmonary alveolar proteinosis (PAP) confirmed on open lung biopsy. Significant fibrosis in PAP is an extremely rare occurrence with only a few case reports. Our case demonstrated a predominantly central distribution, which has not been described previously.
引用
收藏
页码:242 / 244
页数:3
相关论文
共 12 条
[1]  
Arbiser Zoya K, 2003, Ann Diagn Pathol, V7, P82
[2]   PULMONARY INTERSTITIAL FIBROSIS ASSOCIATED WITH ALVEOLAR PROTEINOSIS [J].
CLAGUE, HW ;
WALLACE, AC ;
MORGAN, WKC .
THORAX, 1983, 38 (11) :865-866
[3]   PULMONARY ALVEOLAR PROTEINOSIS WITH HEMATOLOGIIC DISORDERS [J].
DOYLE, AP ;
BALCERZAK, SP ;
WELLS, CL ;
CRITTENDEN, JO .
ARCHIVES OF INTERNAL MEDICINE, 1963, 112 (06) :940-+
[4]   PULMONARY ALVEOLAR PROTEINOSIS A CORRELATION OF PATHOLOGICAL AND PHYSIOLOGICAL FINDINGS IN A PATIENT FOLLOWED UP WITH SERIAL BIOPSIES OF THE LUNG [J].
FRAIMOW, W ;
CATHCART, RT ;
KIRSHNER, JJ ;
TAYLOR, RC .
AMERICAN JOURNAL OF MEDICINE, 1960, 28 (03) :458-467
[5]   CT features of pulmonary alveolar proteinosis [J].
Holbert, JM ;
Costello, P ;
Li, W ;
Hoffman, RM ;
Rogers, RM .
AMERICAN JOURNAL OF ROENTGENOLOGY, 2001, 176 (05) :1287-1294
[6]   PULMONARY INTERSTITIAL FIBROSIS FOLLOWING ALVEOLAR PROTEINOSIS [J].
HUDSON, AR ;
HALPRIN, GM ;
MILLER, JA ;
KILBURN, KH .
CHEST, 1974, 65 (06) :700-702
[8]   PULMONARY ALVEOLAR PROTEINOSIS WITH INTERSTITIAL INVOLVEMENT [J].
MILLER, PA ;
RAVIN, CE ;
SMITH, GJW ;
OSBORNE, DRS .
AMERICAN JOURNAL OF ROENTGENOLOGY, 1981, 137 (05) :1069-1071
[9]  
Mori T, 1996, Nihon Rinsho, V54, P353
[10]   PULMONARY ALVEOLAR PROTEINOSIS [J].
ROSEN, SH ;
CASTLEMAN, B ;
LIEBOW, AA ;
ENZINGER, FM ;
HUNT, RTN .
NEW ENGLAND JOURNAL OF MEDICINE, 1958, 258 (23) :1123-1142