The biogenesis, traffic, and function of the cystic fibrosis transmembrane conductance regulator

被引:37
作者
Jilling, T [1 ]
Kirk, KL [1 ]
机构
[1] UNIV ALABAMA, DEPT PHYSIOL & BIOPHYS, BIRMINGHAM, AL 35294 USA
来源
INTERNATIONAL REVIEW OF CYTOLOGY - A SURVEY OF CELL BIOLOGY, VOL 172 | 1997年 / 172卷
关键词
cystic fibrosis; genetic disease; ion channels; membrane traffic; protein processing;
D O I
10.1016/S0074-7696(08)62361-X
中图分类号
Q2 [细胞生物学];
学科分类号
071009 ; 090102 ;
摘要
引用
收藏
页码:193 / 241
页数:49
相关论文
共 50 条
[31]   Defects in processing and trafficking of cystic fibrosis transmembrane conductance regulator [J].
Kunzelmann, K ;
Nitschke, R .
EXPERIMENTAL NEPHROLOGY, 2000, 8 (06) :332-342
[32]   A Proteomic Survey of the Cystic Fibrosis Transmembrane Conductance Regulator Surfaceome [J].
Iazzi, Melissa ;
Sadeghi, Sara ;
Gupta, Gagan D. .
INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES, 2023, 24 (14)
[33]   Defects in processing and trafficking of the cystic fibrosis transmembrane conductance regulator [J].
Skach, WR .
KIDNEY INTERNATIONAL, 2000, 57 (03) :825-831
[34]   Expression of cystic fibrosis transmembrane conductance regulator in paracervical ganglia [J].
Su, Meng ;
Guo, Yong ;
Zhao, Yingying ;
Korteweg, Christine ;
Gu, Jiang .
BIOCHEMISTRY AND CELL BIOLOGY, 2010, 88 (04) :747-755
[35]   Control of epithelial Na+ conductance by the cystic fibrosis transmembrane conductance regulator [J].
Kunzelmann, K ;
Schreiber, R ;
Nitschke, R ;
Mall, M .
PFLUGERS ARCHIV-EUROPEAN JOURNAL OF PHYSIOLOGY, 2000, 440 (02) :193-201
[36]   Cystic Fibrosis Transmembrane Conductance Regulator Folding Mutations Reveal Differences in Corrector Efficacy Linked to Increases in Immature Cystic Fibrosis Transmembrane Conductance Regulator Expression [J].
Peters, Kathryn W. ;
Gong, Xiaoyan ;
Frizzell, Raymond A. .
FRONTIERS IN PHYSIOLOGY, 2021, 12
[37]   Activation of the Cystic Fibrosis Transmembrane Conductance Regulator by the Flavonoid Quercetin Potential Use as a Biomarker of ΔF508 Cystic Fibrosis Transmembrane Conductance Regulator Rescue [J].
Pyle, Louise C. ;
Fulton, Jennifer C. ;
Sloane, Peter A. ;
Backer, Kyle ;
Mazur, Marina ;
Prasain, Jeevan ;
Barnes, Stephen ;
Clancy, J. P. ;
Rowe, Steven M. .
AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY, 2010, 43 (05) :607-616
[38]   Paediatric Thoracic Imaging in Cystic Fibrosis in the Era of Cystic Fibrosis Transmembrane Conductance Regulator Modulation [J].
O'Regan, Patrick W. ;
Stevens, Niamh E. ;
Logan, Niamh ;
Ryan, David J. ;
Maher, Michael M. .
CHILDREN-BASEL, 2024, 11 (02)
[39]   Cystic Fibrosis Transmembrane Conductance Regulator-Modifying Medications: The Future of Cystic Fibrosis Treatment [J].
Pettit, Rebecca S. .
ANNALS OF PHARMACOTHERAPY, 2012, 46 (7-8) :1065-1075
[40]   Cystic Fibrosis Transmembrane Conductance Regulator Channel Dysfunction in Non-Cystic Fibrosis Bronchiectasis [J].
Bienvenu, Thierry ;
Sermet-Gaudelus, Isabelle ;
Burgel, Pierre-Regis ;
Hubert, Dominique ;
Crestani, Bruno ;
Bassinet, Laurence ;
Dusser, Daniel ;
Fajac, Isabelle .
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2010, 181 (10) :1078-1084