The biogenesis, traffic, and function of the cystic fibrosis transmembrane conductance regulator

被引:37
|
作者
Jilling, T [1 ]
Kirk, KL [1 ]
机构
[1] UNIV ALABAMA, DEPT PHYSIOL & BIOPHYS, BIRMINGHAM, AL 35294 USA
来源
INTERNATIONAL REVIEW OF CYTOLOGY - A SURVEY OF CELL BIOLOGY, VOL 172 | 1997年 / 172卷
关键词
cystic fibrosis; genetic disease; ion channels; membrane traffic; protein processing;
D O I
10.1016/S0074-7696(08)62361-X
中图分类号
Q2 [细胞生物学];
学科分类号
071009 ; 090102 ;
摘要
引用
收藏
页码:193 / 241
页数:49
相关论文
共 50 条
  • [1] Structure and function of the cystic fibrosis transmembrane conductance regulator
    Morales, MM
    Capella, MAM
    Lopes, AG
    BRAZILIAN JOURNAL OF MEDICAL AND BIOLOGICAL RESEARCH, 1999, 32 (08) : 1021 - 1028
  • [3] The cystic fibrosis transmembrane conductance regulator and ATP
    Devidas, S
    Guggino, WB
    CURRENT OPINION IN CELL BIOLOGY, 1997, 9 (04) : 547 - 552
  • [4] Where Is the Cystic Fibrosis Transmembrane Conductance Regulator?
    Barbry, Pascal
    Marcet, Brice
    Caballero, Ignacio
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2021, 203 (10) : 1214 - 1216
  • [5] Cystic fibrosis and survival to 40 years: a study of cystic fibrosis transmembrane conductance regulator function
    Simmonds, N. J.
    D'Souza, L.
    Roughton, M.
    Alton, E. W. F. W.
    Davies, J. C.
    Hodson, M. E.
    EUROPEAN RESPIRATORY JOURNAL, 2011, 37 (05) : 1076 - 1082
  • [6] Biosynthesis of cystic fibrosis transmembrane conductance regulator
    Pranke, Iwona M.
    Sermet-Gaudelus, Isabelle
    INTERNATIONAL JOURNAL OF BIOCHEMISTRY & CELL BIOLOGY, 2014, 52 : 26 - 38
  • [7] EPIGENETIC REGULATION OF AUTOPHAGY AND CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR (CFTR) FUNCTION IN CYSTIC FIBROSIS
    Amer, A.
    Tazi, M.
    Caution, K.
    PEDIATRIC PULMONOLOGY, 2015, 50 : 285 - 285
  • [8] THE CYSTIC-FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR
    RIORDAN, JR
    ANNUAL REVIEW OF PHYSIOLOGY, 1993, 55 : 609 - 630
  • [9] Glycosylation and the cystic fibrosis transmembrane conductance regulator
    Scanlin, TF
    Glick, MC
    RESPIRATORY RESEARCH, 2001, 2 (05) : 276 - 279
  • [10] Cystic Fibrosis Transmembrane Conductance Regulator and Pseudomonas
    Zemanick, Edith T.
    Accurso, Frank J.
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2014, 189 (07) : 763 - 765