Purpose of reviewWe discuss the relationship between several factors and the risk of vascular events in patients with Behcet's disease.Recent findingsBehcet's disease, a systemic, chronic relapsing vasculitis, is mainly seen in the Mediterranean area and is typically characterized by recurrent oro-genital ulcers, ocular inflammation, and skin manifestations, including articular, vascular, gastroenteric, and neurological involvement. It is a chronic inflammatory disease with relapses and remissions. The prognosis varies. Behcet's disease can cause venous or arterial lesions. Vascular involvement contributes to the mortality and morbidity associated with Behcet's disease.SummaryThe cause of thrombosis or vascular events in Behcet's disease remains incompletely understood; several factors have been studied with conflicting results. Vasculitis is considered to underlie several clinical manifestations of Behcet's disease.