Anesthetic management for foramen magnum decompression in a patient with Morquio syndrome: a case report

被引:3
作者
Geetha, Lakshminarsimhaiah [1 ]
Radhakrishnan, Muthuchellappan [1 ]
Raghavendra, Biligiri Sridhar [1 ]
Rao, G. S. Umamaheswara [1 ]
Devi, Bhagavatula Indira [2 ]
机构
[1] Natl Inst Mental Hlth & Neurosci, Dept Neuroanesthesia, Bangalore 560029, Karnataka, India
[2] Natl Inst Mental Hlth & Neurosci, Dept Neurosurg, Bangalore 560029, Karnataka, India
关键词
Mucopolysaccharidosis; Difficult airway; Fiberoptic intubation; Cervical myelopathy; Atlantoaxial dislocation; CHILDREN;
D O I
10.1007/s00540-010-0963-9
中图分类号
R614 [麻醉学];
学科分类号
100217 ;
摘要
Morquio syndrome is a hereditary mucopolysaccharide disorder presenting with an abnormality of the craniocervical junction from childhood. We describe an adult patient who presented with Morquio syndrome who had subglottic narrowing of the airway, restrictive pulmonary disease, and mild mitral regurgitation and trivial aortic regurgitation. The anesthetic management of this patient for atlantoaxial stabilization is presented.
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收藏
页码:594 / 597
页数:4
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