Molecular Analysis of Type 1 VWD Mutations: Effects of Mutant: Wild-Type Transfection Ratio and Protein Degradation

被引:0
|
作者
White-Adams, Tara C. [1 ,2 ]
Jacobi, Paula M. [3 ]
Haberichter, Sandra L. [4 ]
Di Paola, Jorge A. [1 ,2 ]
机构
[1] Univ Colorado, Aurora, CO USA
[2] Childrens Hosp Colorado, Aurora, CO USA
[3] BloodCtr Wisconsin, Milwaukee, WI USA
[4] Med Coll Wisconsin, Dept Pediat, Milwaukee, WI 53226 USA
关键词
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:544 / 544
页数:1
相关论文
共 50 条
  • [21] Protein engineering of nitrile hydratase activity of papain: Molecular dynamics study of a mutant and wild-type enzyme
    Reddy, SY
    Kahn, K
    Zheng, YJ
    Bruice, TC
    JOURNAL OF THE AMERICAN CHEMICAL SOCIETY, 2002, 124 (44) : 12979 - 12990
  • [22] SURVIVAL AND EFFECTS OF WILD-TYPE, MUTANT, AND RECOMBINANT STREPTOMYCES IN A SOIL ECOSYSTEM
    WANG, ZM
    CRAWFORD, DL
    POMETTO, AL
    RAFII, F
    CANADIAN JOURNAL OF MICROBIOLOGY, 1989, 35 (05) : 535 - 543
  • [23] Pathogenic Aβ production by heterozygous PSEN1 mutations is intrinsic to the mutant protein and not mediated by conformational hindrance of wild-type PSEN1
    Kurth, Vanessa
    Ogorek, Isabella
    Muench, Carolina
    Lopez-Rios, Javier
    Ousson, Solenne
    Lehmann, Sandra
    Nieweg, Katja
    Roebroek, Anton J. M.
    Pietrzik, Claus U.
    Beher, Dirk
    Weggen, Sascha
    JOURNAL OF BIOLOGICAL CHEMISTRY, 2023, 299 (08)
  • [24] Growth analysis of wild-type and photomorphogenic-mutant tomato plants
    Kerckhoffs, LHJ
    Sengers, MMT
    Kendrick, RE
    PHYSIOLOGIA PLANTARUM, 1997, 99 (02) : 309 - 315
  • [25] Analysis of nuclear actin by overexpression of wild-type and actin mutant proteins
    Enikö Kokai
    Henning Beck
    Julia Weissbach
    Franziska Arnold
    Daniela Sinske
    Ulrike Sebert
    Gerd Gaiselmann
    Volker Schmidt
    Paul Walther
    Jan Münch
    Guido Posern
    Bernd Knöll
    Histochemistry and Cell Biology, 2014, 141 : 123 - 135
  • [26] Functional analysis of mutant and wild-type Drosophila origin recognition complex
    Chesnokov, I
    Remus, D
    Botchan, M
    PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 2001, 98 (21) : 11997 - 12002
  • [27] Molecular modeling of wild-type and antifolate resistant mutant Plasmodium falciparum DHFR
    Delfino, RT
    Santos, OA
    Figueroa-Villar, JD
    BIOPHYSICAL CHEMISTRY, 2002, 98 (03) : 287 - 300
  • [28] ULTRASTRUCTURAL AND BIOCHEMICAL-ANALYSIS OF PIGMENTATION IN MUTANT AND WILD-TYPE AXOLOTLS
    EPP, LG
    FROST, SK
    AMERICAN ZOOLOGIST, 1982, 22 (04): : 929 - 929
  • [29] Molecular dynamics simulations of wild-type and mutant NEU transmembrane domains.
    van der Ende, BM
    Davis, JH
    Sharom, FJ
    BIOPHYSICAL JOURNAL, 2000, 78 (01) : 330A - 330A
  • [30] TRANSFECTION OF WILD-TYPE AND FANCONI ANEMIA-LIKE MOUSE LYMPHOMA MUTANT-CELLS BY ELECTROPORATION
    FRASER, D
    DIATLOFFZITO, C
    MOUSTACCHI, E
    MUTATION RESEARCH, 1991, 263 (03): : 165 - 171