Primary angiitis of the CNS (PACNS)

被引：5

作者：

Rollnik, JD ^{[1
]}

Brandis, A

Dehghani, K

Bufler, J

Lorenz, M

Heidenreich, F

Donnerstag, F

机构：

[1] Hannover Med Sch, Neurol Klin Klin Neurophysiol, D-30623 Hannover, Germany

[2] Hannover Med Sch, Inst Neuropathol, Hannover, Germany

[3] Hannover Med Sch, Neurochirurg Klin, Hannover, Germany

[4] Hannover Med Sch, Inst Neuroradiol, Hannover, Germany

来源：

NERVENARZT | 2001年 / 72卷 / 10期

关键词：

primary angiitis of the CNS; PACNS; vasculitis; biopsy; diagnosis;

D O I：

10.1007/s001150170038

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

Primary angiitis of the CNS (PACNS) is a rare inflammatory disease affecting middle-aged patients. The angiitis is focal and segmental in distribution, involving small and medium-sized leptomeningeal and intracranial vessels. The most frequent presenting symptoms are headaches, focal neurologic deficits, and confusion. In addition, aphasia, neuropsychological deficits, and seizures may occur. The paper presents a review of the literature. In addition,a typical case of PACNS is presented. This case demonstrates that diagnosis of PACNS is difficult and brain biopsy is essential to confirm it.

引用

页码：798 / 801

页数：4

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