Malignant B cell non-Hodgkin's lymphoma of the larynx in children with Wiskott Aldrich syndrome

被引:17
作者
Palenzuela, G
Bernard, F
Gardiner, Q
Mondain, M [1 ]
机构
[1] CHU Montpellier, Serv ORL, ENT Dept, F-34295 Montpellier 5, France
[2] CHU Montpellier, Hop Arnaud de Villeneuve, Serv Pediat 3, Serv Oncol Pediat, F-34295 Montpellier 5, France
[3] Univ Dundee, ENT Dept, Dundee, Scotland
关键词
child; Wiskott Aldrich syndrome; non-Hodgkin's lymphoma; laryngeal lymphoma; malignancy;
D O I
10.1016/S0165-5876(03)00155-1
中图分类号
R76 [耳鼻咽喉科学];
学科分类号
100213 ;
摘要
A 15 years old male with a primary diagnosis of Wiskott Aldrich syndrome presented a laryngeal B cell lymphoma associated with Epstein-Barr virus. A chemotherapy and a radiotherapy were started in association with an endoscopic debulking of the tumor. The child died of respiratory failure secondary to a lung infection. The incidence of NHL (non-Hodgkin's lymphoma) of laryngeal origin in infants is extremely tow and to our knowledge it has never been found in Wiskott Aldrich syndrome. (C) 2003 Elsevier Ireland Ltd. All rights reserved.
引用
收藏
页码:989 / 993
页数:5
相关论文
共 15 条
  • [1] CACHIN Y, 1978, TUMEURS CERVICO FACI, P29
  • [2] Cavalot AL, 2001, J LARYNGOL OTOL, V115, P324
  • [3] NON-HODGKINS-LYMPHOMA OF THE LARYNX IN CHILDREN
    COHEN, SR
    THOMPSON, JW
    SIEGEL, SE
    [J]. ANNALS OF OTOLOGY RHINOLOGY AND LARYNGOLOGY, 1987, 96 (04) : 357 - 361
  • [4] WISKOTT-ALDRICH SYNDROME - AN IMMUNOLOGIC DEFICIENCY DISEASE INVOLVING AFFERENT LIMB OF IMMUNITY
    COOPER, MD
    CHASE, HP
    LOWMAN, JT
    KRIVIT, W
    GOOD, RA
    [J]. AMERICAN JOURNAL OF MEDICINE, 1968, 44 (04) : 499 - &
  • [5] MALIGNANT-LYMPHOMA IN PATIENTS WITH THE WISKOTT-ALDRICH SYNDROME
    COTELINGAM, JD
    WITEBSKY, FG
    HSU, SM
    BLAESE, RM
    JAFFE, ES
    [J]. CANCER INVESTIGATION, 1985, 3 (06) : 515 - 522
  • [6] FILIPOVICH AH, 1992, CANCER RES, V52, pS5465
  • [7] Long-term survival following non-Hodgkin's lymphoma arising in Wiskott-Aldrich syndrome
    Gilson, D
    Taylor, RE
    [J]. CLINICAL ONCOLOGY, 1999, 11 (04) : 283 - 285
  • [8] GINAHRT TD, 1980, CANCER, V46, P1683
  • [9] HADDAD E, 1999, HEMATOLOGIE, P15
  • [10] HADDAD E, 1999, ENCYCL MED CHIR, P15