Crazy Paving Pattern of the Lung

被引：3

作者：

Fisser, C. ^{[1
,2
]}

Hamer, O. W. ^{[3
,4
]}

Eiber, R. ^{[5
]}

Pfeifer, M. ^{[1
,2
]}

Lerzer, C. ^{[2
]}

机构：

[1] Univ Klin Regensburg, Klin & Poliklin Innere Med 2, Regensburg, Germany

[2] Fachklin Lungenerkrankungen Donaustauf, Abt Pneumol, Donaustauf, Germany

[3] Univ Klin Regensburg, Inst Rontgendiagnost, Regensburg, Germany

[4] Fachklin Lungenerkrankungen Donaustauf, Abt Radiol, Donaustauf, Germany

[5] Sana Kliniken Landkreises Cham, Abt Anasthesiol, Cham, Germany

来源：

PNEUMOLOGIE | 2019年 / 73卷 / 01期

关键词：

PULMONARY ALVEOLAR PROTEINOSIS;

D O I：

10.1055/a-0767-7960

中图分类号：

R56 [呼吸系及胸部疾病];

学科分类号：

摘要：

Pulmonary alveolar proteinosis (PAP) is a rare pulmonary disease. PAP results from impaired surfactant clearance. In adults, autoimmune pulmonary alveolar proteinosis is present in 90-95% of the cases. In 5-10%, other etiologies such as toxins and dust exposure, hematological disorders and infections have to be considered. Men between 30-60 years are commonly affected. Typical symptoms are cough, dyspnea and alteration in ventilatory function. CT scan of the lung is characterised by a crazy paving pattern. In serological testing, granulocyte macrophage colony-stimulation factor can be identified in most patients with autoimmune pulmonary alveolar proteinosis. Whole-lung lavage remains the therapy of choice. In the current case, treatment with whole-lung lavage resulted in clinical and functional improvement.

引用

页码：49 / 53

页数：5

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