How many people have sickle cell disease in the UK?

被引：44
作者：
Dormandy, Elizabeth [1 ]
James, John [1 ]
Inusa, Baba [2 ]
Rees, David [3 ,4 ]
机构：
[1] Sickle Cell Soc, 54 Stn Rd, London NW10 4UA, England
[2] Guys & St Thomas NHS Fdn Trust, Evelina London Childrens Healthcare, London, England
[3] Kings Coll London, Dept Mol Haematol, London, England
[4] Kings Coll NHS Fdn Trust, London, England
来源：
JOURNAL OF PUBLIC HEALTH | 2018年 / 40卷 / 03期
关键词：
blood and immune disorders; epidemiology; genetics; CHILDREN; ENGLAND; TRENDS;
D O I：
10.1093/pubmed/fdx172
中图分类号：
R1 [预防医学、卫生学];
学科分类号：
1004 ; 120402 ;
摘要：
Background Sickle Cell Disease (SCD) is now one of the most common serious genetic condition in England. There is no reliable estimate of the total number of people living with SCD in the UK, to support commissioners and providers of services for people with SCD. Aim To obtain reliable data on the total number of people living with SCD in the UK in 2016. Method Information was requested from all national databases known to hold information on the number of people living with SCD in the UK. The information from each data source was first reviewed to estimate likely inaccuracies and then combined to provide a best estimate of people living with SCD in the UK. Conclusion This process indicated there are are about 14000 people living with SCD in the UK. This is equivalent to 1 in 4600 people.
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收藏
页码：E291 / E295
页数：5
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