Prolonged remission of severe Cushing syndrome without adrenalectomy in an infant with McCune-Albright syndrome

被引:14
|
作者
Gillis, David [1 ]
Roesler, Ariel [2 ]
Hannon, Tamara S. [5 ]
Koplewitz, Benjamin Z. [3 ]
Hirsch, Harry J. [4 ]
机构
[1] Hadassah Hebrew Univ Med Ctr, Dept Pediat, Pediat Endocrine Unit, Jerusalem, Israel
[2] Hadassah Hebrew Univ Med Ctr, Dept Endocrinol & Metab, Jerusalem, Israel
[3] Hadassah Hebrew Univ Med Ctr, Dept Med Imaging, Jerusalem, Israel
[4] Shaare Zedek Med Ctr, Dept Pediat, Jerusalem, Israel
[5] Childrens Hosp Pittsburgh, Dept Pediat, Div Endocrinol, Pittsburgh, PA 15213 USA
来源
JOURNAL OF PEDIATRICS | 2008年 / 152卷 / 06期
关键词
D O I
10.1016/j.jpeds.2008.01.037
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
A 4 month-old girl presented with severe Cushing syndrome caused by McCune-Albright syndrome. After undergoing 19 months of pharmacologic suppression of cortisol production, she has been in clinical remission for more than 6 years. Adrenalectomy may be avoidable even in severe cases of Cushing syndrome associated with McCune-Albright syndrome.
引用
收藏
页码:882 / 884
页数:3
相关论文
共 50 条
  • [1] Cushing Syndrome in the McCune-Albright Syndrome
    Brown, Rebecca J.
    Kelly, Marilyn H.
    Collins, Michael T.
    JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM, 2010, 95 (04): : 1508 - 1515
  • [2] Cushing Syndrome in patients with McCune-Albright Syndrome
    Aziz, Mariana
    Ciaccio, Marta
    Guercio, Gabriela
    HORMONE RESEARCH IN PAEDIATRICS, 2023, 96 (SUPPL 2): : 114 - 115
  • [3] Recovery of Cushing syndrome revealing McCune-Albright syndrome
    Halioui-Louhaichi, S.
    Dridi, Y.
    Azzabi, O.
    Selmi, I.
    Fetni, I.
    Siala, N.
    Maherzi, A.
    ARCHIVES DE PEDIATRIE, 2016, 23 (01): : 61 - 65
  • [4] Ketoconazole treatment for Cushing syndrome in McCune-Albright syndrome
    Vong, Cecilia Heng
    Forest, Maguelone
    Nicolino, Marc
    JOURNAL OF PEDIATRICS, 2009, 154 (03): : 467 - 468
  • [5] Infant cholestasis in McCune-Albright syndrome
    EL-Rifai, N
    Lumbroso, S
    Cartigny, M
    Weill, J
    Sultan, C
    Gottrand, F
    ACTA PAEDIATRICA, 2004, 93 (01) : 141 - 141
  • [6] A CASE OF NEONATAL MCCUNE-ALBRIGHT SYNDROME WITH CUSHING SYNDROME AND HYPERTHYROIDISM
    YOSHIMOTO, M
    NAKAYAMA, M
    BABA, T
    UEHARA, Y
    NIIKAWA, N
    ITO, M
    TSUJI, Y
    ACTA PAEDIATRICA SCANDINAVICA, 1991, 80 (10): : 984 - 987
  • [7] Cushing syndrome and other endocrinopathies in a boy with McCune-Albright syndrome
    Brandsma, Annelies
    Boot, Annemieke
    HORMONE RESEARCH, 2006, 65 : 78 - 78
  • [8] Ketoconazole treatment for Cushing syndrome in McCune-Albright syndrome Reply
    Gillis, David
    Rosler, Ariel
    Koplewitz, Benjamin Z.
    Hannon, Tamara S.
    Hirsch, Harry J.
    JOURNAL OF PEDIATRICS, 2009, 154 (03): : 468 - 469
  • [9] THE MCCUNE-ALBRIGHT SYNDROME
    LORINI, R
    LARIZZA, D
    CISTERNINO, M
    BELUFFI, G
    SEVERI, F
    ACTA PAEDIATRICA SCANDINAVICA, 1984, 73 (06): : 860 - 860
  • [10] MCCUNE-ALBRIGHT SYNDROME
    SCHWINDINGER, WF
    LEVINE, MA
    TRENDS IN ENDOCRINOLOGY AND METABOLISM, 1993, 4 (07): : 238 - 242