We report a very rare case of an accessory pseudophallus with an accessory pseudoscrotum detected during a routine second-trimester antenatal sonographic scan. Classification In 1928, Schnider classified various forms of double penis into 3 main types: (1) diphallia of the glans alone, (2) bifid diphallia, and (3) complete diphallia or double penis. Vilanova and Raventos(1) added a fourth type called pseudodiphallia. According to Hollowell et al, (2) pseudodiphallia was classified into 2 types: complete and incomplete. Definition According to Vilanova and Raventos,(1) pseudodiphallus is a normal penis associated with an indication or a rudiment of an atrophic penis existing independently of the normal penis. This anomaly could be found alone or with other concomitant anomalies such as intestinal anomalies (imperforate anus(3-5) and esophageal atresia(6)), duplication and extrophy of the bladder,(7) vertebral anomalies,(6) cloacal extrophy,(7) and scrotal anomalies.(4) Background and Prevalence Pseudodiphallia occurs in 1 per 5.5 million live births.(3,4,8) The first case, on a cadaver, was reported in 1609 by Wecker in Bologna, Italy. Only about 80 cases have been reported since then, but all these cases were discovered postnatally.(8)
