Malignant perivascular epithelioid cell tumor (PEComa) of uterus: A case report with literature review

被引：0

作者：

Noh, Joseph J. ^{[1
]}

Hong, Sir-Yeon ^{[1
]}

Kim, Byeong-gie ^{[1
]}

机构：

[1] Sungkyunkwan Univ, Samsung Med Ctr, Dept Obstet & Gynecol, Sch Med, 81 Irwon Ro, Seoul 06351, South Korea

来源：

EUROPEAN JOURNAL OF GYNAECOLOGICAL ONCOLOGY | 2020年 / 41卷 / 04期

关键词：

Perivascular epithelioid cell tumor (PEComa); Uterus; Adjuvant chemotherapy; Vincristine; Sirolimus; Dacarbazine; MTOR INHIBITION; SOFT-TISSUE; TEMSIROLIMUS; ACTIVATION; SIROLIMUS; NEOPLASMS;

D O I：

10.31083/j.ejgo.2020.04.5305

中图分类号：

R73 [肿瘤学];

学科分类号：

100214 ;

摘要：

Perivascular epithelioid cell tumor (PEComa) is a rare mesenchymal neoplasm involving various organs. Approximately 70 cases of gynecologic PEComas have been reported in the literature. Due to the paucity of cases, there is no definite treatment regimen established. We describe disease progression in a case of uterine PEComa with pulmonary metastasis in a 37-year-old woman who had been treated with surgery and various regimens of adjuvant treatment including vincristine, ifosfamide, cisplatin, sirolimus, doxorubicin, olaratumab, pazopanib and dacarbazine. Adequate management and prognosis still seem inconclusive and further case reports with randomized trials are needed to delineate the nature of this neoplasm.

引用

页码：495 / 499

页数：5

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