Origins of Cystic Fibrosis Lung Disease

[11] State of the Art: Why do the lungs of patients with cystic fibrosis become infected and why can't they clear the infection? [J]. RESPIRATORY RESEARCH, 2003, 4 (08)

[12] Personalized Medicine in Cystic Fibrosis Dawning of a New Era [J]. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2012, 186 (07) : 593 - 597

[13] Abnormal surface liquid pH regulation by cultured cystic fibrosis bronchial epithelium [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 2003, 100 (26) : 16083 - 16088

[14] Cystic fibrosis: a mucosal immunodeficiency syndrome [J]. NATURE MEDICINE, 2012, 18 (04) : 509 - 519

[15] Differences in Disease Expression Between Primary Ciliary Dyskinesia and Cystic Fibrosis With and Without Pancreatic Insufficiency [J]. CHEST, 2014, 145 (04) : 738 - 744

[16] Cystic Fibrosis Foundation, Cystic Fibrosis Foundation Patient Registry: 2021 annual data report

[17] MEDICAL PROGRESS Airway Mucus Function and Dysfunction [J]. NEW ENGLAND JOURNAL OF MEDICINE, 2010, 363 (23) : 2233 - 2247

[18] Tracheomalacia Is Associated With Lower FEV1 and Pseudomonas Acquisition in Children With CF [J]. PEDIATRIC PULMONOLOGY, 2014, 49 (10) : 960 - 970

[19] Bioelectric Characterization of Epithelia from Neonatal CFTR Knockout Ferrets [J]. AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY, 2013, 49 (05) : 837 - 844

[20] On a remarkable bacteriolytic element found in tissues and secretions. [J]. PROCEEDINGS OF THE ROYAL SOCIETY OF LONDON SERIES B-CONTAINING PAPERS OF A BIOLOGICAL CHARACTER, 1922, 93 (653) : 306 - 317

[11] State of the Art: Why do the lungs of patients with cystic fibrosis become infected and why can't they clear the infection? [J]. RESPIRATORY RESEARCH, 2003, 4 (08)

[12] Personalized Medicine in Cystic Fibrosis Dawning of a New Era [J]. AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2012, 186 (07) : 593 - 597

[13] Abnormal surface liquid pH regulation by cultured cystic fibrosis bronchial epithelium [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 2003, 100 (26) : 16083 - 16088

[14] Cystic fibrosis: a mucosal immunodeficiency syndrome [J]. NATURE MEDICINE, 2012, 18 (04) : 509 - 519

[15] Differences in Disease Expression Between Primary Ciliary Dyskinesia and Cystic Fibrosis With and Without Pancreatic Insufficiency [J]. CHEST, 2014, 145 (04) : 738 - 744

[16] Cystic Fibrosis Foundation, Cystic Fibrosis Foundation Patient Registry: 2021 annual data report

[17] MEDICAL PROGRESS Airway Mucus Function and Dysfunction [J]. NEW ENGLAND JOURNAL OF MEDICINE, 2010, 363 (23) : 2233 - 2247

[18] Tracheomalacia Is Associated With Lower FEV1 and Pseudomonas Acquisition in Children With CF [J]. PEDIATRIC PULMONOLOGY, 2014, 49 (10) : 960 - 970

[19] Bioelectric Characterization of Epithelia from Neonatal CFTR Knockout Ferrets [J]. AMERICAN JOURNAL OF RESPIRATORY CELL AND MOLECULAR BIOLOGY, 2013, 49 (05) : 837 - 844

[20] On a remarkable bacteriolytic element found in tissues and secretions. [J]. PROCEEDINGS OF THE ROYAL SOCIETY OF LONDON SERIES B-CONTAINING PAPERS OF A BIOLOGICAL CHARACTER, 1922, 93 (653) : 306 - 317