Origins of Cystic Fibrosis Lung Disease

被引：432
作者：
Stoltz, David A. [1 ,2 ,5 ,6 ]
Meyerholz, David K. [3 ]
Welsh, Michael J. [1 ,2 ,4 ]
机构：
[1] Univ Iowa, Dept Internal Med, Iowa City, IA 52242 USA
[2] Univ Iowa, Dept Mol Physiol & Biophys, Iowa City, IA 52242 USA
[3] Univ Iowa, Dept Pathol, Iowa City, IA 52242 USA
[4] Univ Iowa, Howard Hughes Med Inst, Iowa City, IA 52242 USA
[5] Univ Iowa, Roy J & Lucille Carver Coll Med, Iowa City, IA 52242 USA
[6] Univ Iowa, Dept Biomed Engn, Iowa City, IA 52242 USA
来源：
NEW ENGLAND JOURNAL OF MEDICINE | 2015年 / 372卷 / 04期
关键词：
TRANSMEMBRANE CONDUCTANCE REGULATOR; AIRWAY SURFACE DEHYDRATION; CFTR-KNOCKOUT FERRETS; SUBMUCOSAL GLANDS; MUCOCILIARY TRANSPORT; BICARBONATE SECRETION; BRONCHIAL EPITHELIUM; PORCINE MODEL; NEWBORN PIGS; LIQUID PH;
D O I：
10.1056/NEJMra1300109
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
[No abstract available]
引用
收藏
页码：351 / 362
页数：12
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