Congenital Diaphragmatic Hernia Repair in a Patient With Pallister-Killian Mosaic Syndrome and Left Ventricular Hypoplasia

被引：1
|
作者：
Kostyk, Piotr [1 ]
Salik, Irim [2 ]
机构：
[1] Westchester Med Ctr, Anesthesiol, Valhalla, NY 10595 USA
[2] Westchester Med Ctr, Anesthesia, Valhalla, NY USA
来源：
CUREUS JOURNAL OF MEDICAL SCIENCE | 2022年 / 14卷 / 03期
关键词：
pulmonary hypertension; craniofacial dysmorphism; left ventricular hypoplasia; pallister-killian syndrome; congenital diaphragmatic hernia; PULMONARY-HYPERTENSION; INFANTS;
D O I：
10.7759/cureus.23095
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
We present the case of a two-week-old infant with congenital diaphragmatic hernia (CDH) and PallisterKillian mosaic syndrome (PKS) for CDH repair. We discuss the pathophysiologic findings of both conditions and the resulting anesthetic challenges from their interplay.
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页数：4
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