Hepatobiliary and Gastrointestinal Involvement in Langerhans Cell Histiocytosis-Spectrum of Three Cases

被引:0
作者
Pratap, Thara [1 ]
Jalal, Muhammed Jasim Abdul [2 ]
Rashmi, R. [3 ]
Gopalakrishnabhakthan, Anupama [4 ]
Vishnu, A. K. [1 ]
机构
[1] VPS Lakeshore Hosp, Dept Radiol, Kochi, Kerala, India
[2] VPS Lakeshore Hosp, Dept Internal Med & Rheumatol, Nettoor PO,NH 47 Byepass, Kochi 682040, Kerala, India
[3] VPS Lakeshore Hosp, Dept Pathol, Kochi, Kerala, India
[4] VPS Lakeshore Hosp, Dept Med Oncol, Kochi, Kerala, India
关键词
histiocytosis; Langerhans cell; nodular; gastrointestinal; alanine aminotransferase; LIVER;
D O I
10.1055/s-0041-1735505
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
Langerhans cell histiocytosis (ICH) is a rare group of disorder, due to clonal neoplastic proliferation of dendritic cells in the bone marrow expressing a Langerhans cell phenotype.(1) This disease particularly affects the pediatric age group and young adults and often presents with skin rashes, lung infiltrates, and bone lesions. It can also manifest with endocrine dysfunction and hematopoietic disorders. Involvement of gastrointestinal tract is very rare. Herein, we present a spectrum of three cases with gastrointestinal involvement.
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收藏
页码:670 / 677
页数:8
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