An Unusual Case of Ectopic ACTH Syndrome Due to Primary Retroperitoneal Carcinoid

被引:3
作者
Kasaliwal, Rajeev [1 ]
Malhotra, Gaurav [2 ]
Lila, Anurag [1 ]
Bandgar, Tushar [1 ]
Shah, Nalini S. [1 ]
机构
[1] Seth GS Med Coll, Dept Endocrinol, Mumbai, Maharashtra, India
[2] Tata Mem Hosp, Bhabha Atom Res Ctr, Radiat Med Ctr, Bombay 400012, Maharashtra, India
关键词
Ectopic ACTH syndrome; Ga-68 DOTANOC PET/CT; I-131-MIBG; retroperitoneal carcinoid; CUSHINGS-SYNDROME;
D O I
10.1097/RLU.0000000000000687
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
A 37-year-old woman with clinical and biochemical features of ectopic adrenocorticotropic hormone (ACTH) syndrome underwent Ga-68 DOTANOC PET/CT to localize the source of ectopic ACTH secretion. The images showed 35 x 45-mm retroperitoneal mass with significantly increased tracer uptake. Plasma-free metanephrines and serum chromogranin levels were normal. Whole-body I-131-MIBG scan including the retroperitoneal mass did not show any abnormal uptake. On excision, histopathology of this paravertebral abdominal mass revealed carcinoid tumor. We suggest the use of Ga-68 DOTANOC PET/CT as a first-line imaging modality for localization of source of ACTH secretion in ectopic ACTH syndrome.
引用
收藏
页码:364 / 367
页数:4
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