Pulmonary Hypertension Associated With Hemoglobinopathies Prevalent But Overlooked

被引:70
作者
Farmakis, Dimitrios [1 ]
Aessopos, Athanasios [1 ]
机构
[1] Univ Athens, Sch Med, Dept Internal Med, Laiko Hosp, GR-11527 Athens, Greece
关键词
hypertension; pulmonary; pulmonary arterial hypertension; hemoglobinopathies; beta-thalassemia; sickle cell disease; SICKLE-CELL-DISEASE; BETA-THALASSEMIA; HEART-DISEASE; NITRIC-OXIDE; PSEUDOXANTHOMA ELASTICUM; ARTERIAL-HYPERTENSION; CARDIAC INVOLVEMENT; RISK-FACTOR; INTERMEDIA; ACTIVATION;
D O I
10.1161/CIRCULATIONAHA.110.988089
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
[No abstract available]
引用
收藏
页码:1227 / 1232
页数:6
相关论文
共 48 条
[1]   Cardiac status in well-treated patients with thalassemia major [J].
Aessopos, A ;
Farmakis, D ;
Hatziliami, A ;
Fragodimitri, C ;
Karabatsos, F ;
Joussef, J ;
Mitilineou, E ;
Diamanti-Kandaraki, E ;
Meletis, J ;
Karagiorga, M .
EUROPEAN JOURNAL OF HAEMATOLOGY, 2004, 73 (05) :359-366
[2]   Pulmonary hypertension in β-thalassemia. [J].
Aessopos, A ;
Farmakis, D .
COOLEY'S ANEMIA EIGHTH SYMPOSIUM, 2005, 1054 :342-349
[3]   Thalassernia heart disease - A comparative evaluation of Thalassemia major and Thalassemia intermedia [J].
Aessopos, A ;
Farmakis, D ;
Deftereos, S ;
Tsironi, A ;
Tassiopoulos, S ;
Moyssakis, I ;
Karagiorga, M .
CHEST, 2005, 127 (05) :1523-1530
[4]   PULMONARY-HYPERTENSION AND RIGHT HEART-FAILURE IN PATIENTS WITH BETA-THALASSEMIA-INTERMEDIA [J].
AESSOPOS, A ;
STAMATELOS, G ;
SKOUMAS, V ;
VASSILOPOULOS, G ;
MANTZOURANI, M ;
LOUKOPOULOS, D .
CHEST, 1995, 107 (01) :50-53
[5]   Cardiac involvement in thalassemia intermedia: a multicenter study [J].
Aessopos, A ;
Farmakis, D ;
Karagiorga, M ;
Voskaridou, E ;
Loutradi, A ;
Hatziliami, A ;
Joussef, J ;
Rombos, J ;
Loukopoulos, D .
BLOOD, 2001, 97 (11) :3411-3416
[6]   Elastic tissue abnormalities resembling pseudoxanthoma elasticum in β thalassemia and the sickling syndromes [J].
Aessopos, A ;
Farmakis, D ;
Loukopoulos, D .
BLOOD, 2002, 99 (01) :30-35
[7]   Arterial calcifications in β-thalassemia [J].
Aessopos, A ;
Samarkos, M ;
Voskaridou, E ;
Papaioannou, D ;
Tsironi, M ;
Kavouklis, E ;
Vaiopoulos, G ;
Stamatelos, G ;
Loukopoulos, D .
ANGIOLOGY, 1998, 49 (02) :137-143
[8]   Heart disease in thalassemia intermedia: a review of the underlying pathophysiology [J].
Aessopos, Athanasios ;
Kati, Maria ;
Farmakis, Dimitrios .
HAEMATOLOGICA-THE HEMATOLOGY JOURNAL, 2007, 92 (05) :658-665
[9]   Endothelial function and arterial stiffness in sickle-thalassemia patients [J].
Aessopos, Athanasios ;
Farmakis, Dimitrios ;
Tsironi, Maria ;
Diamanti-Kandarakis, Evanthia ;
Matzourani, Marina ;
Fragodimiri, Christina ;
Hatziliami, Antonia ;
Karagiorga, Markisia .
ATHEROSCLEROSIS, 2007, 191 (02) :427-432
[10]   Cardiac involvement in sickle β-thalassemia [J].
Aessopos, Athanasios ;
Farmakis, Dimitrios ;
Trompoukis, Christos ;
Tsironi, Maria ;
Moyssakis, Ioannis ;
Tsaftarides, Panagiotis ;
Karagiorga, Markisia .
ANNALS OF HEMATOLOGY, 2009, 88 (06) :557-564