Pulmonary Hypertension Associated With Hemoglobinopathies Prevalent But Overlooked

被引:70
作者
Farmakis, Dimitrios [1 ]
Aessopos, Athanasios [1 ]
机构
[1] Univ Athens, Sch Med, Dept Internal Med, Laiko Hosp, GR-11527 Athens, Greece
关键词
hypertension; pulmonary; pulmonary arterial hypertension; hemoglobinopathies; beta-thalassemia; sickle cell disease; SICKLE-CELL-DISEASE; BETA-THALASSEMIA; HEART-DISEASE; NITRIC-OXIDE; PSEUDOXANTHOMA ELASTICUM; ARTERIAL-HYPERTENSION; CARDIAC INVOLVEMENT; RISK-FACTOR; INTERMEDIA; ACTIVATION;
D O I
10.1161/CIRCULATIONAHA.110.988089
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
[No abstract available]
引用
收藏
页码:1227 / 1232
页数:6
相关论文
共 48 条
  • [1] Cardiac status in well-treated patients with thalassemia major
    Aessopos, A
    Farmakis, D
    Hatziliami, A
    Fragodimitri, C
    Karabatsos, F
    Joussef, J
    Mitilineou, E
    Diamanti-Kandaraki, E
    Meletis, J
    Karagiorga, M
    [J]. EUROPEAN JOURNAL OF HAEMATOLOGY, 2004, 73 (05) : 359 - 366
  • [2] Pulmonary hypertension in β-thalassemia.
    Aessopos, A
    Farmakis, D
    [J]. COOLEY'S ANEMIA EIGHTH SYMPOSIUM, 2005, 1054 : 342 - 349
  • [3] Thalassernia heart disease - A comparative evaluation of Thalassemia major and Thalassemia intermedia
    Aessopos, A
    Farmakis, D
    Deftereos, S
    Tsironi, A
    Tassiopoulos, S
    Moyssakis, I
    Karagiorga, M
    [J]. CHEST, 2005, 127 (05) : 1523 - 1530
  • [4] PULMONARY-HYPERTENSION AND RIGHT HEART-FAILURE IN PATIENTS WITH BETA-THALASSEMIA-INTERMEDIA
    AESSOPOS, A
    STAMATELOS, G
    SKOUMAS, V
    VASSILOPOULOS, G
    MANTZOURANI, M
    LOUKOPOULOS, D
    [J]. CHEST, 1995, 107 (01) : 50 - 53
  • [5] Cardiac involvement in thalassemia intermedia: a multicenter study
    Aessopos, A
    Farmakis, D
    Karagiorga, M
    Voskaridou, E
    Loutradi, A
    Hatziliami, A
    Joussef, J
    Rombos, J
    Loukopoulos, D
    [J]. BLOOD, 2001, 97 (11) : 3411 - 3416
  • [6] Elastic tissue abnormalities resembling pseudoxanthoma elasticum in β thalassemia and the sickling syndromes
    Aessopos, A
    Farmakis, D
    Loukopoulos, D
    [J]. BLOOD, 2002, 99 (01) : 30 - 35
  • [7] Arterial calcifications in β-thalassemia
    Aessopos, A
    Samarkos, M
    Voskaridou, E
    Papaioannou, D
    Tsironi, M
    Kavouklis, E
    Vaiopoulos, G
    Stamatelos, G
    Loukopoulos, D
    [J]. ANGIOLOGY, 1998, 49 (02) : 137 - 143
  • [8] Heart disease in thalassemia intermedia: a review of the underlying pathophysiology
    Aessopos, Athanasios
    Kati, Maria
    Farmakis, Dimitrios
    [J]. HAEMATOLOGICA-THE HEMATOLOGY JOURNAL, 2007, 92 (05): : 658 - 665
  • [9] Endothelial function and arterial stiffness in sickle-thalassemia patients
    Aessopos, Athanasios
    Farmakis, Dimitrios
    Tsironi, Maria
    Diamanti-Kandarakis, Evanthia
    Matzourani, Marina
    Fragodimiri, Christina
    Hatziliami, Antonia
    Karagiorga, Markisia
    [J]. ATHEROSCLEROSIS, 2007, 191 (02) : 427 - 432
  • [10] Cardiac involvement in sickle β-thalassemia
    Aessopos, Athanasios
    Farmakis, Dimitrios
    Trompoukis, Christos
    Tsironi, Maria
    Moyssakis, Ioannis
    Tsaftarides, Panagiotis
    Karagiorga, Markisia
    [J]. ANNALS OF HEMATOLOGY, 2009, 88 (06) : 557 - 564