Metastasized angiosarcoma of the spleen in a 2-year-old girl

被引:15
作者
den Hoed, IDM
Granzen, B
Aronson, DC
Pauwels, P
de Kraker, J
van Heurn, LWE
机构
[1] Univ Hosp Maastricht, Dept Paediat Surg Paediat & Pathol, NL-6202 AZ Maastricht, Netherlands
[2] Univ Amsterdam, Acad Med Ctr, Emma Childrens Hosp AMC, Dept Paediat Surg & Paediat Oncol, NL-1105 AZ Amsterdam, Netherlands
关键词
angiosarcoma; chemotherapy; hepatic metastases; spleen;
D O I
10.1080/08880010590964228
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
Primary angiosarcoma of the spleen is rare and the prognosis is very poor The authors present a 2-year-old girl with spontaneous rupture of splenic angiosarcoma. At diagnosis there were liver metastases. After splenectomy she received chemotherapy with ifosfamide, vincristine, and actinomycine D combined with a partial liver resection. She remained in complete remission over 2 years from diagnosis.
引用
收藏
页码:387 / 390
页数:4
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