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Retroperitoneal Spindle Cell Rhabdomyosarcoma With Compression Features in a 48-Year-Old Male: A Case Report
被引:0
作者:
Ramesh, Krishna
[1
]
Jangda, Anzal
[2
]
Annam, Swetha
[3
,4
]
Mangrio, Marium A.
[5
]
Sajeev, Krishna
[6
]
Kumar, Anish
[7
]
Qayyum, Mahrukh
[8
]
Jamali, Momal
[9
]
Yahya Jr, Allahyar
[10
]
Mehbub, Hummaz
[10
]
机构:
[1] Ramaiah Med Coll, Internal Med, Bangalore, India
[2] Ziauddin Univ, Internal Med, Karachi, Pakistan
[3] Osmania Med Coll & Hosp, Pulm Med, Hyderabad, Pakistan
[4] Bhaskar Med Coll, Internal Med, Hyderabad, Pakistan
[5] Sukkur Civil Hosp, Med & Surg, Sukkur, Pakistan
[6] Govt Med Coll Kannur, Internal Med, Pariyaram, India
[7] Ghulam Muhammad Mahar Med Coll Hosp, Internal Med, Sukkur, Pakistan
[8] Allama Iqbal Med Coll, Internal Med, Lahore, Pakistan
[9] Dow Univ Hlth Sci, Internal Med, Karachi, Pakistan
[10] Akhtar Saeed Med & Dent Coll, Gen Surg, Lahore, Pakistan
关键词:
embryonal rhabdomyosarcoma;
retroperitoneal mass;
spindle cell rhabdomyosarcoma;
p-rms;
rhabdomyosarcoma (rms);
rms;
ADULT;
D O I:
10.7759/cureus.29622
中图分类号:
R5 [内科学];
学科分类号:
1002 ;
100201 ;
摘要:
Spindle cell rhabdomyosarcoma (SC-RMS) is an unprecedented version of embryonal rhabdomyosarcomas (RMSs) that emerges from the mesenchyme with the capacity to differentiate into skeletal muscle cells. Retroperitoneal RMS is extremely rare in the adult population. We present the case of a primary spindle cell retroperitoneal RMS with compression features. Investigation-based diagnosis of RMS is difficult due to the lack of specificity of clinical findings. Radiology does not help in making an accurate diagnosis. Surgical removal of the tumor followed by chemotherapy and radiotherapy is the best possible treatment for RMS in adults. SC-RMS has a poor long-term prognosis. To our knowledge, such cases of retroperitoneal SC-RMS compressing the abdominal viscera and resulting in hydroureteronephrosis have never been reported before.
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